Cavernous Lymphangioma of the Digits: A Rare Cause of Macrodactyly

@#Cavernous lymphangioma is a congenital malformation of lymphatic system causing dilated lymphatic sinuses that involve the skin and subcutaneous tissues. This was an interesting case of dystrophic macrodactyly of the left ring and little finger in a 18-month-old girl who presented with swollen and sausage like fingers deformity which turned out to be an isolated cavernous lymphangioma. This tumor, although rare to occur in the extremeties, must be differentiated from other congenital vascular lesions of the hand that include arteriovenous malformations and hemangiomas. Diagnosis should be solely based on histopathological analysis of the excised tissue mass. Surgical excision is usually necessary for satisfactory functional and cosmetic outcome.

Child with Mediastinal cavernous lymphangioma.

Mediastinal cavernous lymphangioma is a benign rare lesion originating from lymphatic system. It is usually asymptomatic. We have presented a 2 year old male child with fever for seven days. Opacity was found in chest X-ray in the upper part of right hemithorax, merged with the mediastinum.CT scan of chest was performed, which revealed a large, lobulated, smoothly marginated non-enhancing, low density, mediastinal mass, involving right half, extending from root of neck. Finally, pathological examination of the surgical sample indicated ?Cavernous lymphangioma’.

Resección laparoscópica de linfangioma cavernoso retroperitoneal residual / Laparoscopic resection of a residual retroperitoneal cavernous lymphangioma

Objetivo: Presentar el caso de una paciente con linfangioma cavernoso diagnosticado incidentalmente y tratado quirúrgicamente, primero por laparotomía y después, para su resolución final, mediante laparoscopia. Se discuten las ventajas de la cirugía miniinvasiva como método adyuvante en la resección del linfangioma residual después de una laparotomía extensa. Sede: Hospital de tercer nivel. Diseño: Presentación del caso y revisión de la literatura. Descripción del caso: Mujer de 43 años, en la cual se documentó masa quística aparentemente dependiente del ovario derecho, con marcadores tumorales para cáncer ovárico normales. Se programó para salpingoclasia y resección de quiste ovárico, por incisión Pfannenstiel, encontrando un quiste gigante de origen retroperitoneal, que se extendía desde el hueco pélvico hasta el abdomen superior. Fue extirpado casi en su totalidad, debido a la extensión de la tumoración, excepto en la porción pancreatoduodenal y retrohepática, ya que al intentar abordar esta zona, inició con sangrado transoperatorio y se desconocían las relaciones del tumor con estos órganos. Se difirió la resección de esta porción residual para complementar su estudio por imágenes e histopatología y llevarlo a cabo en un segundo tiempo quirúrgico. La tomografía postoperatoria no mostró dependencia pancreatoduodenal, biliar o vascular. Al mes, se programó para la resección laparoscópica del tumor residual. El reporte histopatológico fue linfangioma cavernoso en ambos casos. Conclusiones: El tratamiento para los linfangiomas retroperitoneales es la resección completa. La cirugía miniinvasiva es una alternativa útil, ventajosa y mejor aceptada por los pacientes en algunas reoperaciones planeadas, donde inicialmente se realizó cirugía abierta.

Objective: To present the case of a woman with cavernous lymphangioma incidentally diagnosed and surgically treated, first through laparotomy and later, for its final resolution, through laparoscopy. We discuss the advantages of mini-invasive surgery as an adjuvant method for the resection of a residual lymphangioma after extensive laparotomy. Setting: Third level health care hospital. Design: Case presentation and review of the literature. Case description: A 43-year-old woman, in whom a cystic mass, apparently depending on the right ovary was documented; tumor markers for ovarian cancer were normal. She was programmed to undergo salpingoplasty and resection of the ovarian cyst, through Pfannenstiel incision. During surgery a giant cyst of retroperitoneal origin was found, which extended from the pelvic hole to the upper abdomen. It was resected almost totally due to the extension of the tumor, except for the pancreatoduodenal and retrohepatic region, because, when attempting to approach this area, transoperative bleeding started and we did not know the relations of the tumor with these organs. The resection of this residual portion was deferred to be able to complement the diagnosis with imaging and histopathology studies and perform the resection at a second surgical time. Postoperative tomography revealed no pancreatoduodenal, biliary, or vascular dependence. After 1 month, the patient was programmed for laparoscopic resection of the residual tumor. The histopathological report corresponded to cavernous lymphangioma in both situations. Conclusions: Treatment of retroperitoneal lymphangiomas consists of complete resection. Mini-invasive surgery is a useful, valuable option and a better accepted alternative by patients in some planned re-operations where initially open surgery had been performed.

Cavernous Lymphangioma Arising in the Chest Wall 19 Years after Excision of a Cystic Hygroma

Lymphangioma is a congenital malformation of the lymphatic system and is thought to result from the failure of the lymphatic system to connect with the venous system. Lymphangioma of the chest wall is a very rare disease entity, and only a few cases have ever been documented in the literature. To the best of our knowledge, there have been few cases of recurrent cavernous lymphangioma after surgical excision of a cystic hygroma on the same side of the chest wall. Here, we report a case of a cavernous lymphangioma of the chest wall in a patient who had undergone surgical excision of a cystic hygroma 19 years earlier.

Splenic Cavernous Lymphangioma Mimicking Splenic Hemangioma

Lymphangioma of the spleen is a rare benign neoplasm with clinical manifestations ranging from insignificant incidental findings to large, symptomatic cystic masses requiring surgical intervention. We report a case of splenic cavernous lymphangioma mimicking splenic hemangioma. A 59-year-old woman presented with left upper quadrant pain and epigastric discomfort. Computed tomography showed a 9.5x8 cm high attenuated mass with relatively homogenous enhancement in the spleen. The initial impression was a splenic hemangioma. The patient underwent splenectomy. Gross pathologic examination revealed a 9.5x6.8x9 cm-sized fairly well circumscribed soft mass. Histologically, the tumor was composed of dilated lymphatic vessels, which contained homogenous eosinophilic material. The Final diagnosis was cavernous lymphangioma of the spleen. Herein, we report a case of splenic cavernous lymphangioma mimicking splenic hemangioma and also review the existing literature.

Solitary Pulmonary Lymphangioma in an Adult: A Brief Case Report

Solitary pulmonary lymphangiomas are extremely rare. We report here on an unique case of solitary pulmonary lymphangioma in an adult. A well-circumscribed, 6 cm-sized, pleural based lesion with fluid attenuation was found in a 50-year-old Korean male. He had no previous history of disease or trauma. The wedge-resected lung revealed an ill-demarcated lesion with multiple microscopic cysts and the cystic walls had loose intervening stroma.

Successful Weaning after Diaphragmatic Plication in an Infant with Phrenic Nerve Palsy Resulting from Removal of Cavernous Lymphangioma / 대한구급학회지

Phrenic nerve palsy is a well-known complication following cardiac surgery in children. The incidence is approximately 1~2%. In infants and young children, it often causes a life-threatening respiratory distress. They must be treated with mechanical ventilation in the ICU. Many patients with phrenic nerve injury who is impossible to wean from a ventilator are candidates of diaphragmatic plication. Diaphragmatic plication is performed to restore the normal pulmonary parenchymal volume by replacing the diaphragm to its proper location. This is a case of 2-months-old infant who had phrenic nerve palsy after the removal of cavernous lymphangioma of the chest. He underwent 4 operations to remove the mass and to have pericardiotomy. We tried to wean him from the ventilator but failed several times in the ICU. After 4th operation, right diaphragmatic elevation was noted from the chest X ray. Phrenic nerve palsy was confirmed with fluoroscopy and he underwent diaphragmatic plication on 42 days after his 4th operation. Three days after the diaphragmatic plication, weaning was successfully carried out.

Orbital Cavernous Lymphangioma with Intracranial Extension: Case Report

Lymphangioma is a rare benign developmental vascular tumor that may be found in orbit, skull and elsewhere in head and neck. Few cases of extension of this benign but insidious tumor posteriorly out of the bony orbital cavity have been reported. The patient was 40-year-old man complaining of proptosis of right eye for one month. Physical examination revealed severe right exophthalmus, impairment of eyeball movement in all directions. Visual acuity was much impaired and he could percept only light with right eye. CT and MRI scans showed intraconal and extraconal involvement of ill-defined, heterogenous mass with extension of the tumor posteriorly beyond the orbital cavity involving right frontal and temporal lobe, skull and subcutaneous tissue. The tumor was subtotally removed via orbito-frontal approach without damaging vital neural and orbital component. Then, orbital roof reconstruction and cranioplasty were done with resin. Successful surgical removal of lymphangioma is very difficult due to its severe infiltration to surrounding tissue and tendency to bleed during debulking. We report a rare case of orbital cavernous lymphangioma with intracranial extension treated with surgical decompression, with review of literatures.

A case of cavernous lymphangioma in mediastinum

Cavernous lymphangioma in mediastinum is a rare congenital malformation of lymphatic system and is caused by lack of adequate drainage from the sequestrated lymphatic vessels to the venous system due to insufficiency or atresia of the efferent lymphatic channels The authors experienced 10 month-old male patient with cavernous lymphangioma in mediastinum documented by chest CT and open biopsy The review of the literature was made briefly.

Cavernous Lymphangioma of the Scrotum: Report of A Case / 대한비뇨기과학회지

A 13-year old boy was seen for progressive enlargement of a right scrotal mass that had been present since early childhood. Scrotal mass was excised and consisted of a well demarcated multinodular cystic soft mass. Pathology was characteristic of cavernous lymphangioma. Lymphangiomas are benign tumors of congenital origin, occurring about 95% of the lesion at neck and axilla. Their scrotal location is quite uncommon. Treatment consists of surgical excision. Unless completely removed, recurrences are common.