The application value of CT and MRI on children’s vein of Galen malformation / 实用放射学杂志

Objective To investigate the clinical application value of CT and MRI on the children’s vein of Galen malformation (VGAM).Methods CT and MRI images of 10 children cases with VGAM were analyzed retrospectively.Results CT and MRI find-ings:10 cases with dilatation of the vein of Galen,8 cases with straight sinus dilation,6 cases with dilation of confluence sinus,and 6 cases with other sinus dilatation.Blood supply vessels:basilar artery in 6 cases,posterior cerebral artery in 2 cases,anterior cerebral artery in 1 case and other vascular in 1 case.Complications:bleeding in 4 cases,thrombosis in 2 cases,and calcification in 2 cases. Conclusion CT and MRI can confirm the diagnosis of children’s VGAM,and abnormal blood-supply vessels.CT has advantages of observation of calcifications,and MRI has advantages of observation of hemorrhage and thrombosis.

Malformación aneurismática de la vena de Galeno: Reporte de un caso / Vein of Galen aneurysmal malformation: a case report

Las malformaciones aneurismáticas de la vena de Galeno representan aproximadamente un tercio de todas las malformaciones vasculares intracraneales en la edad pediátrica; sin embargo, existe poca referencia en el medio. Los pacientes con este tipo de malformación presentaban altas tasas de morbimortalidad hasta la década de los noventa; desde entonces el desarrollo en las técnicas de diagnóstico prenatal y de terapia endovascular han permitido modificar el pronóstico de esta población. Se describe el caso de un paciente en quien se hizo diagnóstico prenatal, se realizó tratamiento con terapia endovascular a los cuatro meses de vida, y se obtuvieron buenos resultados. Se hace enfásis en el diagnóstico temprano y en la prevención de secuelas a través de una intervención oportuna.

Aneurysmal malformations of the vein of Galen represent approximately one third of all intracranial vascular malformations in children. However, in our country we have few references. Patients with this type of malformation had high morbi-mortality rates until the early nineties; since then, the development of techniques of prenatal diagnosis and endovascular therapy have allowed to modify the prognosis of these patients. We describe the case of a patient in whom prenatal diagnosis of aneurysmal malformation of the vein of Galen was made, and was managed at four months of age with endovascular therapy with good results. We emphasize on early diagnosis and prevention of sequelae through appropriate intervention.