ABSTRACT
Supernumerary teeth are regarded as an anomalous increase in the number of naturally occurring teeth. Multiple supernumerary teeth can be seen in association with syndromes such as Cleidocranial dysplasia, Gardner’s syndrome, Fabry-Anderson syndrome and Ehlers-Danlos syndrome. Non-syndromic occurrence however is a rarity and very few reported cases exist. Th e exact etiopathogenesis of the condition remains unknown, but several theories have been proposed, the most popular one being “hyperactivity of dental lamina.” When present, supernumeraries often pose a problem to the normal development and eruption of the neighboring dentition. Most of them are accidental fi ndings on radiographs, which also happens to be the most reliable tool in early diagnosis of this abnormality. We describe a case of 28-year-old male having 10 supernumerary teeth with non-syndromic association, which were diagnosed during routine radiographic evaluation.
Subject(s)
Adult , Cleidocranial Dysplasia/complications , Humans , Male , Review Literature as Topic , Tooth, Supernumerary/diagnosis , Tooth, Supernumerary/epidemiology , Tooth, Supernumerary/etiology , Tooth, Supernumerary/diagnostic imagingABSTRACT
La disostosis cleidocraneal es una enfermedad esqueletal rara que se caracteriza por retardo en la osificación cranel, hipoplaisa o aplasia clavicular y anomalías dentarias. En esta publicación se mostrarán dos casos en que se involucra la genética y las enfermedades del sistema óseo y dentario, corresopndientes a dos miembros de la misma familia. Se detallan la etiología y patogenia, así como los hallazgos clínicos y radiográficos.
Subject(s)
Humans , Male , Female , Adolescent , Middle Aged , Tooth, Impacted/surgery , Tooth, Impacted , Cleidocranial Dysplasia/complications , Cleidocranial Dysplasia/therapy , Cleidocranial Dysplasia/etiology , Cleidocranial Dysplasia/pathologyABSTRACT
CONTEXTO: A isquemia do membro superior não é tão comum quanto a isquemia do membro inferior, mas quando não diagnosticada ou diagnosticada de forma errada determina grave seqüela e até perda da extremidade. RELATO DE CASO: O caso de uma paciente com isquemia do membro superior, devida a disostose cleidocraniana, é apresentado. Esta é uma causa extremamente rara de compressão do segmento arterial subclávio-axilar que evoluiu para trombose arterial. Somente dois casos foram previamente relatados na literatura com esta condição e nesta forma de apresentação.