ABSTRACT
Abstract Although many anatomical variations may be encountered in children with double outlet right ventricle, coexistence of levo-malposed great vessels and left juxtaposed atrial appendages is uncommonly observed. This case report underlines the rarity of this anatomical combination and its clinical significance along with the surgical management in an infant.
Subject(s)
Humans , Infant , Child , Transposition of Great Vessels/diagnostic imaging , Double Outlet Right Ventricle/surgery , Double Outlet Right Ventricle/diagnostic imaging , Atrial Appendage/surgery , Atrial Appendage/diagnostic imaging , Heart Defects, Congenital/surgery , Heart Defects, Congenital/diagnostic imaging , ArteriesSubject(s)
Humans , Female , Adult , Pulmonary Valve Stenosis/diagnostic imaging , Double Outlet Right Ventricle/diagnostic imaging , Heart Septal Defects, Ventricular/diagnostic imaging , Aorta/diagnostic imaging , Pulmonary Valve Stenosis/physiopathology , Double Outlet Right Ventricle/physiopathology , Echocardiography , Magnetic Resonance Spectroscopy , Radiography, Thoracic , Diagnosis, Differential , Electrocardiography , Heart Septal Defects, Ventricular/physiopathologySubject(s)
Aortopulmonary Septal Defect/diagnosis , Aortopulmonary Septal Defect/surgery , Aortopulmonary Septal Defect/diagnostic imaging , Double Outlet Right Ventricle/diagnosis , Double Outlet Right Ventricle/surgery , Double Outlet Right Ventricle/diagnostic imaging , Echocardiography, Transesophageal , Humans , InfantABSTRACT
Intra-operative trans-esophageal echocardiography (TEE) is an important monitoring and diagnostic tool used during surgery for repair of congenital heart disease. In several studies,TEE has been shown to provide additional intra-cardiac anatomic information. Its ability to be used intra- operatively before and after cardiac repair makes it a unique tool. Before TEE was available for intra-operative use, significant residual abnormalities were frequently not detected. The result was often substantial post-operative morbidity and mortality and sometimes the need for re-operation. According to practice guidelines established by the Society of Cardiovascular Anesthesiologists and the American Society of Anesthesiologists, there is strong evidence for the usefulness of TEE in surgery for congenital heart disease because it significantly improves the clinical outcome of these patients. Before surgical correction, TEE helps confirm diagnosis and spot any additional lesion, while after the surgical correction, it provides baseline parameters for comparison after the surgical correction.