ABSTRACT
A case of true inverse Duane's retraction syndrome, bilateral inverse globe retraction syndrome apparently due to abnormal innervation, is the subject of this clinical report.
Subject(s)
Duane Retraction Syndrome/physiopathology , Eye Movements/physiology , Follow-Up Studies , Humans , Infant , Male , Oculomotor Muscles/physiopathology , Ophthalmologic Surgical Procedures/methods , Time FactorsABSTRACT
Objetivos: Descrever as características de 41 pacientes acompanhados no departamento de Motilidade Ocular. Local: Hospital das Clínicas da Faculdade de Medicina da USP. Pacientes e Métodos: Estudo retrospectivo de 41 casos de Síndrome de Duane quanto às características clínicas oculares. Resultados: 22 pacientes do sexo masculino e 19 do feminino. Predominância do tipo I (75,6 por cento) e de acometimento do olho esquerdo (70,7 por cento). 92,6 por cento dos casos era bilateral. 24,4 por cento dos pacientes foram submetidos à cirurgia, com 70 por cento de bons resultados. Conclusão: Nosso estudo condiz com o relato na literatura quanto às características clínicas desta síndrome.
Subject(s)
Humans , Male , Female , Infant , Child, Preschool , Child , Adolescent , Adult , Ocular Motility Disorders , Duane Retraction Syndrome/congenital , Duane Retraction Syndrome/epidemiology , Duane Retraction Syndrome/physiopathology , Retrospective StudiesABSTRACT
Inverse Duane's retraction syndrome is very uncommon. Congenital cases are even more unusual. A 6-year-old girl with convergent squint along with severe restriction on abduction is described. On attempted abduction, a narrowing of the palpebral fissure, upshoot and retraction of the eyeball were observed. Brain and orbit MRI demonstrated no intracranial or intraorbital mass, fracture, or entrapment of the medial rectus. Forced duction test was strongly positive. The primary lesion was found to be a tight medial rectus with shortening and soft tissue contracture. Surgical tenotomy of the medial rectus led to successful postoperative motility, but some limitation at full adduction and abduction persisted. This is a case reported with congenital medial rectus shortening, suggesting that this condition may be one of the etiologies of the rare inverse Duane's retraction syndrome.