ABSTRACT
No abstract available.
Subject(s)
Child, Preschool , Female , Humans , Flow Cytometry , Hydroa Vacciniforme/diagnosis , Immunophenotyping , Lymphocytosis/complications , Lymphoma/diagnosis , Receptors, Antigen, T-Cell, gamma-delta/genetics , STAT3 Transcription Factor/genetics , Sequence Analysis, DNA , Skin/metabolism , T-Lymphocytes/metabolismABSTRACT
Se presenta caso de mujer de 14 años que consultó por úlceras orales y lesiones cutáneas de tipo vesicular, papular y algunas con evolución a úlcerocostras de centro necrótico, hemorrágico y de variadas formas y tamaños, distribuidas principalmente en áreas fotoexpuestas como rostro y extremidades superiores e inferiores. La anatomía patológica confirmó linfoma tipo hidroa vacciniforme atípico, considerado primer caso descrito y publicado en Paraguay.
A 14 year old female consulted with oral ulcers and skin lesions like vesicles and papules, some of them are ulcers and crusting with a necrotic and hemorrhagic center, the shape and size of every lesion is different, mainly they are presented in sun-exposed areas like the face, arms and legs. The histopathological finding confirms the atypical hidro vaccinifome-like lymphoma, considered first report and published in Paraguay.