ABSTRACT
The modern concept of some embryological structures found as dispersed cells at the retroperitoneal region, is to be considered as a great group of structures with similar embryological origin that can be divided in various anatomical and functional group. A case of a malignant extra-adrenal retroperitoneal paraganglioma is described in a 14 year-old man who presented an episode of hematuria following a history of trauma. A computed tomography was performed and showed a solid mass in lower pole of the left kidney. A magnetic resonance imaging examination was later indicated. Because of the persistence of the mass, a surgical exploration was performed and the tumor was removed. The pathological examination demonstrated a malignant paraganglioma. These tumors are rare and difficult to diagnose pre-operatively. The prognosis is poor and the best results reported are around 3 years survival
Subject(s)
Humans , Male , Adolescent , Kidney , Paraganglioma/diagnosis , Paraganglioma/history , Retroperitoneal Neoplasms/diagnosis , Magnetic Resonance SpectroscopyABSTRACT
Os paragangliomas extra-adrenais constituem um grupo raro de doenças, porém assumem dimensäo maior quando analisados em suas múltiplas facetas de apresentaçäo clínica. A trajetória histórica destes tumores, revela num passado näo täo longínquo, as dificuldades para o reconhecimento e correto diagnóstico dos mesmos. E, principalmente, o temor da abordagem cirúrgica, decorrente do alto grau de complicaçöes operatórias imediatas e tardias. A experiência na conduta e terapêutica de vinte casos destes tumores em um periodo de 35 anos é revista e analisada, objetivando comparar os dados do Departamento de Cirurgia de Cabeça e Pesco13o do Hospital A. C. Camargo da Fundaçäo Antonio Prudente com os obtidos e relatados pela literatura mundial.