RESUMEN
Jarcho Levin syndrome is a rare genetic disorder characterized by malformations of the vertebrae at different levels of the spine and ribs. We present a case of Jarcho Levin Syndrome diagnosed prenatally and was associated with renal abnormalities
Asunto(s)
Humanos , Femenino , Riñón/anomalías , Anomalías Múltiples , Cardiopatías Congénitas , Hernia DiafragmáticaRESUMEN
Pregnancy in non-communicating rudimentary horn is extremely rare and unpredictable in women who have had a vaginal delivery. It carries grave consequences for the mother and fetus. The pregnancy usually terminates by rupturing in second trimester. Therefore, excision of the rudimentary horn and associated fallopian tube advised when diagnosed. We present a case of ruptured rudimentary horn pregnancy where the diagnosis was missed by sonogram at 14 weeks gestation and presented as an acute abdomen and hypovolemic shock. She was managed through emergency lower midline laparotomy together with simultaneous resuscitation. Excision of the rudimentary horn and the right fallopian tube was done. The right ovary was conserved. Postoperative recovery was uneventful