RESUMEN
Introdução: A miastenia gravis (MG) adquirida é uma desordem neuromuscular, que dificulta a transmissão do impulso nervoso e provoca fadiga e fraqueza flutuantes na musculatura ocular, facial, dos membros e respiratória.Casuística: Foram avaliados 51 pacientes com MG, 38 submetidos a tratamento conservador e 13 timectomizados. Métodos: Os instrumentos de QV como Whoqol, qualidade de vida relacionada à saúde (QVRS) SF-36, e depressão ( BDI) foram utilizados.Estatística: Na análise univariada :Wilcoxon, U-Mann-Whitney, Fisher e razão de chance; e na análise multivariada a interação de múltiplos fatores.Resultados: Não houve diferenças significantes entre as terapêuticas em relação aos aspectos clínicos, QV, QVRS e Depressão, através da análise univariada / bem estar nos pacientes...
Introduction: Myasthenia gravis (MG) is an immune mediated neuromuscular disease and orders in nervous impulse transmission. The disease´s clinical characteristics include fatigability and fluctuating weakness of voluntary muscles. Objective: To evaluate the influence of conservative treatment and thymectomy on Qol and clinical response of myasthenic patients.Subjects: Fifty-one myasthenic patients were chosen ; 38 were submitted to conservative therapy and 13 to thymectomy. Methods: Quantitative Qol tools such as Whoqol, SF-36 and BDI were employed to evaluate Qol, HRQol and depression.Statistics: Univariate analysis: Wilcoxon, U-Mann Whitney Fisher tests, Chi-Square.Discriminant analysis was used to analyze the interation of multiple factors.Results: There was no differences between therapeutics groups concerning clinical progress, QoL, HRQoL and depression.The evaluation of multiple parameters pointed to a strong and positive influence of thymectomy in the recovery of the patients...