RESUMEN
We report a case of systemic onset juvenile idiopathic arthritis (SOJIA), the manifestations of which started with fever and skin rash followed by arthritis within neonatal age. Such presentation is extremely rare in the newborn. After exclusion of closely mimicking conditions like congenital infections, neonatal onset multisystem inflammatory disease (NOMID), neonatal; lupus erythematosus (NLE) diagnosis of SOJIA may be entertained even in a neonate where arthritis, fever and rash are the presenting features.
Asunto(s)
Artralgia/diagnóstico , Artritis Juvenil/diagnóstico , Diagnóstico Diferencial , Quimioterapia Combinada , Exantema/diagnóstico , Fiebre/fisiopatología , Estudios de Seguimiento , Humanos , Ibuprofeno/administración & dosificación , Lactante , Dimensión del Dolor , Medición de Riesgo , Índice de Severidad de la Enfermedad , Esteroides/administración & dosificación , Resultado del TratamientoRESUMEN
Juvenile idiopathic arthritis (JIA) is the most common chronic rheumatic disorder of the childhood and is manifested by synovitis with or without systemic features. Secondary vasculitis occurring in response to JIA is reflected clinically on different structures or systems of the body. Here is reported a rare case of systemic onset JIA (SOJIA) with vasculitis leading to peripheral gangrene.