A Rare Case of Oguchi Disease

Oguchi disease is a rare autosomal recessive disorder and the patients present with congenital stationary night blindnesswith slow dark adaptation. Two causative genes have been reported till date. The fundus shows typical golden sheen patternwhich disappears when they remain in a darkened environment for few hours. We report a case of young girl who presentedwith non-progressive night blindness for 10 years and on examination typical fundus finding of Oguchi disease was revealed.The typical golden sheen fundus disappeared after 3 h of dark adaptation. This case is reported for its rarity as only <50 caseshave been reported till date.