1.
An. bras. dermatol
; An. bras. dermatol;95(1): 98-101, Jan.-Feb. 2020. graf
Artículo
en Inglés
| LILACS
| ID: biblio-1088724
RESUMEN
Abstract Pachydermoperiostosis (PDP) or primary hypertrophic osteoarthropathy (PHO) is a rare hereditary disease characterized by digital clubbing, pachydermia, and periostosis. Its pathogenesis is uncertain and the diagnosis is based on clinical and radiological data. A complete form of the syndrome is reported in a male patient with disease onset in adolescence, with compatible clinical and radiological findings, presenting the three cardinal findings as well as other associated manifestations, such as hyperhidrosis and acne.