RESUMEN
A 30-year-old female presented to the surgery outpatient department with complaint of pain in right iliac fossa of one day duration. The pain was associated with nausea and vomiting. On examination, there was localized tenderness and rigidity in the right iliac fossa with positive rebound tenderness. Multiple pigmentation of skin in the abdomen, accessory nipple and scoliosis were also noted. Laboratory investigation revealed neutrophilic leukocytosis. Ultrasound abdomen showed an appendix measuring 4 cm in length and a fibroid uterus. Diagnostic laparoscopy revealed an inflamed appendix with a small blind structure in continuity with the cecum. Operative diagnosis of double appendix was made. Microscopic examination confirmed double appendix with features of appendicitis and periappendicitis in the bigger appendix. We report this case because of it rarity. The surgical resident should be aware of this rare congenital anomaly to avoid missing the other appendix in appendectomy procedures and avoid its medico-legal consequences