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The Korean Journal of Internal Medicine ; : 68-71, 1998.
Artículo en Inglés | WPRIM | ID: wpr-39705

RESUMEN

Wegener's granulomatosis is a distinct form of necrotizing granulomatous vasculitis which usually affects the kidneys and the upper and lower respiratory tracts. Unusual manifestations have also been reported, and these include colitis, urethritis and diabetes insipidus. We describe a case of Wegener's granulomatosis which presented with rapidly progressive renal insufficiency, sudden deafness, red eye, facial palsy, and complicated by uncommon manifestations that were diffuse pulmonary hemorrhage and thrombotic thrombocytopenic purpura.


Asunto(s)
Anciano , Femenino , Humanos , Ciclosporina/uso terapéutico , Hemorragia/complicaciones , Enfermedades Pulmonares/complicaciones , Prednisolona/uso terapéutico , Púrpura Trombocitopénica Trombótica/complicaciones , Granulomatosis con Poliangitis/tratamiento farmacológico , Granulomatosis con Poliangitis/diagnóstico , Granulomatosis con Poliangitis/complicaciones
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