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Keimyung Medical Journal ; : 204-208, 2015.
Artículo en Coreano | WPRIM | ID: wpr-12450

RESUMEN

Hereditary hemorrhagic telangiectasia (HHT), also known as Osler-Weber-Rendu disease, is a rare autosomal dominant vascular disorder involving arteriovenous malformation. HHT is characterized by recurrent epistaxis, cutaneous telangiectasia, and visceral arteriovenous malformations. Hepatic arteriovenous malformation can lead to high output heart failure. We report a case of hereditary hemorrhagic telangiectasia patient who complained dyspnea and edema on both lower extremity.


Asunto(s)
Humanos , Malformaciones Arteriovenosas , Disnea , Edema , Epistaxis , Insuficiencia Cardíaca , Corazón , Extremidad Inferior , Telangiectasia Hemorrágica Hereditaria , Telangiectasia
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