RESUMEN
This article reported 1 cases renal primitive neuroectodermal tumor (PNET) into the inferior veno cava. Before the operation, Enhanced CT showed left renal carcinoma and inferior vena cava tumor thrombus. The maximum diameter of tumor was 12.1 cm, Mayo classification was grade Ⅱ.The patients underwent open radical nephrectomy and inferior vena cava thrombus excision surgery. The pathology showed primitive neuroectodermal tumor. Renal PNET is a rare tumor with high grade.Local and distant metastasis is often found.Renal PNET's clinical manifestations and imaging examinations are not typical. Diagnosis mainly depends on pathological examination results and immunohistochemical technique. At present, surgical treatment combined with radiotherapy and chemotherapy is the main treatment.