RESUMEN
Purpura Fulminans is a severe disorder of acute onset with high morbidity and mortality. It is characterized by DIC with thrombocytopenia, hyofibrinogenemia, hypothrombinemia and anemia. It most often occurs in young with sudden appearance of symmetrical, tender, ecchymotic skin lesions usually involving the lower extremities. An infectious and noninfectious etiology has been proposed. Early recognition and early therapy with appropriate antibiotics and heparin is known to limit both morbidity and mortality. This article reports 5 cases of Purpura Fulminans treated at our centre with review of etiology, pathogenesis, clinical features and treatment.
Asunto(s)
Antibacterianos/uso terapéutico , Anticoagulantes/uso terapéutico , Enfermedades de los Ganglios Basales/etiología , Femenino , Gangrena/etiología , Gangrena/cirugía , Humanos , Lactante , Masculino , Púrpura Fulminante/complicaciones , Púrpura Fulminante/tratamiento farmacológico , Púrpura Fulminante/fisiopatología , Enfermedades de la Piel/etiología , Enfermedades de la Piel/cirugíaRESUMEN
An 8-yr-old female child presented with acute onset of severe pain in the lower limbs and difficulty in walking. Spine MRI showed hyperintense signals on T2 weighted images at T2-T3 level, which was intramedullary in location. The patient was operated and histopathology reported as neuroepithelial cyst. Spinal intramedullary neuroepithelial cysts are rare. Spinal cord compression due to the cyst is very uncommon and because of its rarity the present case is being reported. The clinical features, embryogenesis and literature were reviewed briefly.