An unusual variant of atrophic dermatofibrosarcoma protuberans

Abstract: Dermatofibrosarcoma protuberans is an uncommon neoplasm that is most often seen in young adults. The most common clinical presentation is the protruding form; however, other subtypes are known, such as the atrophic. In 2012 there were only 33 reports of this variant in the literature. Many cases of Dermatofibrosarcoma protuberans in children are only discovered in adulthood because they were not diagnosed early. Due the high morbidity, we raise the need for attention from the dermatologist to recognize uncommon neoplasms in the clinical practice. We report a case of a 15-year-old patient diagnosed with atrophic Dermatofibrosarcoma protuberans on the back.

Syringocystadenoma papilliferum combined with a tubular apocrine adenoma

Abstract: Syringocystadenoma papilliferum and tubular apocrine adenoma are rare benign sweat gland tumors. Syringocystadenoma papilliferum occurs alone or in association with other tumors. Although it is rare, the association of tubular apocrine adenoma with syringocystadenoma papilliferum developing in a sebaceous nevus on the scalp is well documented. However, the co-existence of these two tumors without the background of a sebaceous nevus has not been frequently reported. Syringocystadenoma papilliferum and tubular apocrine adenoma may have a histopathological overlap, but a few cases of a syringocystadenoma papilliferum combined with a tubular apocrine adenoma have been reported. Herein we describe an unusual case of syringocystadenoma papilliferum co-existing with a tubular apocrine adenoma located on the back of a 14-year-old patient in the absence of a pre-existing sebaceous nevus.

Onicomicose e tinea pedis causados por microsporum nanum em paciente portador de hanseníase virchowiana / Onychomycosis and tinea pedis caused by microsporum nanum in patient affected by lepromatous leprosy

O microsporum nanum é dermatófito que raramente causa infecçäo no humana. No entanto, é com freqüência isolado da pele de suínos com ou sem lesöes. Este é um relato de infecçäo humana por M. nanum em paciente procedente de área rural e criador de porcos, com hanseníase virchowiana, que apresentava hiperceratose plantar e onicólise das unhas dos pés e algumas da mäo direita. A cultura para fungos revelou o crescimento do Microsporum nanum a partir de material colhido da regiäo plantar e unhas. Houve regressäo das lesöes da pele e melhora das lesöes ungueais 15 meses após pulsoterapia com itraconazol; entretanto, o exame micológico do raspado das plantas dos pés persistia com presença de hifas de dermatófitos. O Microsporum nanum é referido acometendo várias regiöes da pele glabra e também o couro cabeludo; aos autores entretanto parece ser a primeira citaçäo de acontecimento ungueal

Síndrome de Olmsted: ceratodermia palmoplantar e periorificial mutilante / Olmsted syndrome: mutilating palmoplantar and periorificial keratoderma

Relato de caso de ceratodermia palmoplantar e periorificial mutilante, síndrome de Olmsted, genodermatose rara, de transmissäo possivelmente autossômica dominante. A peculiar localizaçäo de lesöes ceratóticas periorificiais permitiu a individualizaçäo dessa entidade entre várias síndromes clinicamente semelhantes