Unilateral retinitis pigmentosa with hypoplastic tilted disc in other eye

A case of a 32-year-old woman showing pigmentary degeneration of the retina in one eye associated with a hypoplastic tilted disc in fellow eye is presented. Clinical examinations of the patient were performed in order to rule out the various causes which are known to produce fundoscopic features that mimic retinitis pigmentosa. Since these investigations were all negative, the fundus changes were interpreted as a unilateral retinitis pigmentosa. Four years later, the patient was re-examined and the findings were reconfirmed. An association of unilateral retinitis pigmentosa and hypoplastic tilted disc in the other eye can be regarded as exceptional. The possibility of a correlation of the pathogenetic mechanism involved in the development of both conditions is discussed

case of eye lid trauma with retained glass pieces in road traffic accident

We present a case of 33-year-old expatriate woman who presented to us for simple suture removal from her left upper eyelid. She was a front seat passenger and met with a road traffic accident. Primary lid repair was done in nearby poly-clinic. The presence of foreign bodies in her left eyelid was not suspected at the time of primary repair probably due to inadequate history and paucity of clinical findings or lack of imaging studies. The significance of eyelid lacerations in relation to minor initial clinical signs and possible late complications is discussed and suggestions are made for management of all such injuries

Gyrate retinal atrophy of choroid and retina: a case report of 3 members in one family

Hyperornithinemia associated with gyrate atrophy of the choroid and retina is a rare, autosomal recessive disorder resulting from a deficiency of the mitochondrial matrix enzyme, ornithine d-aminotransferase [OAT]. Highest rate of gyrate atrophy is reported in Finland. We report for the first time 3 cases [siblings] in one Omani family in the Gulf, presenting with the classical clinical features and biochemical abnormality of this condition. The available forms of treatments which include treatment with pyridoxine, dietary restriction of arginine and supplementation with creatinine andproline, are known to slow the progress of disease process and help to delay the patient s morbidity, but no form of therapy is found to be unequivocally effective

Cataract surgeries by phaco-sandwich technique through sclerocorneal tunnel, a cohort study in Oman

To evaluate the changes in Preoperative and Postoperative keratometry results and rapid visual rehabilitation in Cataract surgery by our phaco-sandwich technique through the self sealing sclero-corneal tunnel incision without phacoemulsification. 96 eyes of 88 patients with age-related cataracts underwent small incision suture less cataract surgery without phacoemulsification. All eyes were operated by the phaco-sandwich technique through sclerocorneal tunnel with 6 mm frown-shaped external scleral incision. 6 mm single piece PMMA lens was implanted in the capsular bag. Patients were evaluated at 1week, 4 weeks and 12 weeks post-operatively. Ninety six eyes of eighty eight patients were our cohort. During the first post-operative week 8 eyes [8.3%] had uncorrected visual acuity [UCVA] of 6/6. By the end of 12 post-operative weeks, 33 eyes[34.5%] had UCVA of 6/6. 64 [66.7%], 72[75%] and 80[83.3%] eyes had best correctable visual acuity [BCVA] of 6/6 after 4 weeks, 8 weeks and 12 weeks respectively. 64 [66.7%] eyes after 4 weeks, 72 [75%] after 8 weeks and 80 [83%] after 12 weeks had best correctable visual acuity [BCVA] of 6/6. Suture less, small-incision cataract surgery is an economical, safe and effective method of managing cataract cases. This technique also ensures satisfactory and rapid rehabilitation for patients. This procedure can be effectively applied to clear the backlog of cataract-related blindness in places wherein the resources for phaco facilities are not available

Management of severe congenital ptosis autogenous fascia lata brow suspension

To evaluate the functional and cosmetic outcome of brow suspension surgery for unilateral severe congenital ptosis using autogenous fascia lata frontalis sling. Three female and one male patients with severe congenital ptosis were operated for functional and cosmetic reasons. All patients underwent unilateral frontalis sling suspension surgery using autogenous fascia lata. Pre and postoperative photographs were taken. Post-operative lid level, lid contour, lid contact with globe, shape, size, bilateral palpebral fissure symmetry, ptosis recurrence and cosmetic appearance of leg scars were evaluated. Patient's sentiments about the outcome of surgery were also recorded. The age of patients ranged from 17 to 18 years and follow up ranged from 24 to 40 months. All patients achieved satisfactory functional and cosmetic results and expressed high level of satisfaction with surgical outcome. None of our patients had ptosis recurrence, sling extrusion, infection or granuloma formation. Leg scars too had good cosmetic appearance. One patient had a slight under correction of ptosis which was corrected next day morning Under local anaesthesia. Autogenous facia lata is the material of choice for permanent ptosis correction when brow suspension sling is required. It avoids the problems associated with both donor human tissues and synthetic materials such as granuloma extrusion, infection and late failure. Harvesting fascia lata causes no postoperative morbidity

Management of trachomatous cicatricial entropion of the upper eye lid: Our modified technique

Management of trachomatous cicatricial entropion of the upper eye lid presents a difficult problem. Many surgical approaches have been developed to address it. We report the functional and cosmetic results of our modified surgical technique we have developed in the management of trachomatous cicatricial entropion of the upper eye lid. 45 lids of 43 patients having trachomatous cicatricial entropion of upper eye lids were operated by our modified surgical technique in which we combine bilamellar tarsal margin rotation procedure with blepharoplasty. The technique and results were evaluated in a follow up period of up to 40 months. In all 45 upper eye lids, the normal eyelashes rotated away from the surface of the eye and were no longer in contact of the eye ball in all position of gaze. All eyes had adequate lid closure and regular lid margin. No eye had any overhanging baggy fold of skin at operation site. Three eyes had conjuctival granuloma which was excised under local anaesthesia Three eyes needed Diode laser ablation to treat isolated cilia posterior to normal lash line. Three eyes had mild over correction which regressed without any surgical intervention. One lid had segmental necrosis of distal part of eye lid which recovered spontaneously in following days. Our modified technique of combining bilamellar tarsal rotation procedure [BTR] with blepharoplasty appears to be an effective surgical technique in the management of the trachomatous cicatricial entropion of the upper eye lid. It achieves successful anatomical correction along with more acceptable cosmetic appearance