Incontinentia pigmenti: manifestations bucco-dentaires de deux cas dans une meme famille

Incontinentia Pigmenti is a hereditary syndrome affecting primarily the skin and teeth, sometimes accompanied by lesions of the eyes and/or central nervous system. Dental manifestations can include the agenesis of several teeth, and comprehensive dental treatment should take into account the long term rehabilitation of the oral cavity. The case of two sisters with the Incontinentia Pigmenti syndrome is presented in this report