RESUMEN
It is a congenital anomaly related to the persistence of the fetal hyaloidien system and hyperplasty of primary vitreous. The aim of our study is to analyze the epidemiological profile and the diagnostic and therapeutic difficulties of persistent hyperplastic primary vitreous. 13 children [15 eyes] with PHVP treated and followed between 2004 and 2012. Age at admission ranged from 3 months to 14 years. The main call sign was leukocoria in 69.23% of cases; unilateral in 84.6% of our patients. It was an anterior form in 13.3% of eyes, posterior in 6.66% and mixed in 80%. An indication for surgery was raised in 60% of eyes. The postoperative aphakia was corrected with an implant in 77.7% of operated cases. Therapy for amblyopia was performed in all patients. The best visual result: 2/10 and counting fingers in both anterior forms; 1/10 in a posterior form unoperated. Discussion This is an isolated and unilateral affection usually occurs in infants born at term, it is most often revealed by leukocoria. There are 3 clinical forms. The functional prognosis is poor and the PHPV depends on several criteria. Treatment should be tailored to the clinical form. All studies support the value of early diagnosis and early intervention to maximize the visual potential in selected patients. Vision therapy should not be neglected and started quickly in the postoperative period, with appropriate refractive correction of aphakia