[Catecholaminergic polymorphic ventricular tachycardia in adult: a case report]

Catecholaminergic polymorphic ventricular tachycardia [CPVT] is a primary electrical myocardial disease characterized by exercise- and stress-related ventricular tachycardia manifested as syncope and sudden death usually in child and teenager and was rarely described in adults. The management includes betablockade, with the use of implantable cardioverter defibrillators if medical treatment is insufficient. Report a new case of CPVT. We report a case of a 43 years old patient in whom CPVT diagnosis was made during his exploration for palpitations occurring with the effort. Registration Holter ECG revealed several episodes of supraventricular tachycardia and episodes of nocturnal sino-atrial block. The patient had an ICD and betablockade treatment. The TVPC in adult can manifest with attenuated symptoms that can be summarized with palpitations with the exertion. The supraventricular arrhythmias and sinus dysfunction may be at the forefront of Electrocardiographic manifestations. The prognosis of this form seems better than the TVPC of the child. Treatment with betablockade appears to be effective but existing dysfunction sinus facilitates decision to implant the ICD

[Diagnosis of restrictive cardiomyopathy: place of the bidimensional echocardiography]

The restrictive cardiomyopathies are sporadic diseases, their diagnosis is often made tardively. Their main differential diagnosis is the chronic pericardiac constriction. The non invasive diagnostic techniques don't permit always to differentiate this two pathologies of different prognosis and treatment. The target of our work is to specify the place of the echocardiography in the diagnosis of the restrictive cardiomyopathies [RCM]. We collected between January 1993 and January 2005 four patients presenting a RCM. The circumstance of discovery was in any case a global cardiac insufficiency. The echocardiography showed a dilatation of the atrium in all patients, whereas the ventricles were of normal size three times. The study of the endocardium showed an apical fill in all patients, whereas the endocardic calcifications had not been recovered except one time, All patients had a valvular thickening. The systolic function was normal three times over four