[Cardiac involvement in emery dreifuss muscular dystrophy: a case report]

Emery Dreifuss muscular dystrophy [EDMD] is an uncommon hereditary myopathy characterized by 3 symptoms: slow progressive musclar atrophy, muscular contractures and cardiac disease which affect prognosis. We report a 22 year-old patient with EDMD which shows the typical features of the associated dilated cardiomyopathy, ventricular arrhythmia, atrio-ventricular block, atrial standstill then atrial paralysis