RESUMEN
We report a young woman with paraganglionoma arising from the extrahepatic bile duct presenting with acute obstructive jaundice. The patient underwent excision of the gall bladder and extrahepatic bile duct with the tumor, and Roux-en-Y hepaticojejunostomy. She is asymptomatic 9 months later, with normal biochemical investigations and imaging.
Asunto(s)
Adulto , Conductos Biliares Extrahepáticos/patología , Neoplasias del Sistema Biliar/complicaciones , Biopsia con Aguja , Colecistectomía , Colestasis/diagnóstico , Femenino , Estudios de Seguimiento , Humanos , Paraganglioma/complicaciones , Resultado del TratamientoRESUMEN
Von Hippel Lindau disease is rare autosomal dominant disorder. In our patient's family, 4 out of 7 siblings had manifestations of the disease; 3 of those affected had pancreatic lesions with obstructive jaundice in 2 siblings caused by pancreatic cysts is reported for the first time.
Asunto(s)
Adulto , Colestasis/etiología , Enfermedades del Conducto Colédoco/etiología , Femenino , Humanos , Quiste Pancreático/etiología , Enfermedad de von Hippel-Lindau/complicacionesRESUMEN
Thirty patients with severe ulcerative colitis were studied prospectively. Sixty percent (18/30) of severe ulcerative colitis were in remission after mean duration of 9.2 days (range 2-20 days) of intensive intravenous therapy without major side effects of steroids. Factors predicting poor response to medical therapy on admission are: stool frequency > or = 9 per day, pulse rate > or = 120/minute, temperature > or = 38 degrees C, Albumin < or = 2 gm, mucosal tags on plain x-ray abdomen and pancolitis.