RESUMEN
Spinal epidural abscess is one of the rare disease, especially in child. We had experienced a case in 15 months old who was diagnosed by spinal tapping and epidurogram. Total laminectomy of L 1-2 and drainage of the abscess was successfuly performed and he recovered without residual symtoms after operation. A brief review of literatures was made.
Asunto(s)
Niño , Humanos , Lactante , Absceso , Drenaje , Absceso Epidural , Laminectomía , Enfermedades Raras , Punción EspinalRESUMEN
A 38 month old girl was admitted with the episode of anorexia, coughing and dyspnea to St. Mary's hospital on Nov. 9, 1977. She had treated as hepatitis at private clinic for one month before admission, however these symptoms were aggrevated with coughing and progressed dyspnea since a week ago. On physical examination, body temperature 36.8C, body weight 11.7kg, heart rate 150/min, BP 130/110mmHg at right arm, 160/90mmHg at left arm and 100/90mmHg at both legs were noted. The right radial pulse was palpated weakly compare to the left radial and both femoral pulses, which were also weak and bruit were heard on the both right carotid artery and abdominal aorta. On cardiac ausculation, no significant murmur was heard except gallop rhythm. The ECG and chest X-ray revealed the left ventricular enlargement and grade I K-W hypertensive retinopathy was found by fundoscopy. On selective left angiographic study mitral regurgitation(grade IV) was proved, and localized obliteration of the right subclavian artery and left carotid artery and diffuse constrictive narrowing of the thoracic and abdominal aorta at the level from D7 to suprarenal(type III) were seen by sequential ascending and abdominal aortorgaphy. The infrarenal abdominal aorta was also hypoplastic. Tuberculin skin test was strongly positive, and VDRL and LE preparation were negative.
Asunto(s)
Preescolar , Femenino , Humanos , Anorexia , Aorta Abdominal , Brazo , Temperatura Corporal , Peso Corporal , Arterias Carótidas , Tos , Disnea , Electrocardiografía , Estrógenos Conjugados (USP) , Insuficiencia Cardíaca , Frecuencia Cardíaca , Hepatitis , Retinopatía Hipertensiva , Pierna , Examen Físico , Pruebas Cutáneas , Arteria Subclavia , Arteritis de Takayasu , Tórax , TuberculinaRESUMEN
We have experienced 3 cases of Cornelia de Lange syndrome in Korean female infants. They showed typical clinical features of a microbrachycephaly, hirsutism and characteristic face with low forehead bushy eye brows, antimongolian slant, large and depressed briedge of nose, thin protruding lips with down turning of the corners and micrognathia. They also had skeletal abnormalities and chromosomal abnormalities. The diagnosis was established by clinical, laboratory and X-ray findings. The brief review of literature was made.