RESUMEN
Congenital esophageal duplications represent about 15% of digestive tract duplications. We report a 38-year-old man who presented with longstanding heartburn and recent dysphagia. Endoscopy showed communicating tubular duplication of lower esophagus with ulceroproliferative growth at the gastric cardia extending into the lower esophagus. Histology of radical esophagogastrectomy specimen showed poorly differentiated adenocarcinoma of gastric cardia without evidence of Barrett's esophagus.
Asunto(s)
Adenocarcinoma/diagnóstico , Adulto , Biopsia con Aguja , Cardias/patología , Anomalías Congénitas/diagnóstico , Esofagectomía/métodos , Unión Esofagogástrica/patología , Esófago/anomalías , Estudios de Seguimiento , Gastrectomía/métodos , Gastroscopía/métodos , Humanos , Inmunohistoquímica , Masculino , Medición de Riesgo , Neoplasias Gástricas/diagnóstico , Resultado del TratamientoRESUMEN
OBJECTIVE: To assess the effectiveness of surgical treatment for pseudomyxoma peritonei. DESIGN: Retrospective analysis. SETTING: Referral center. PATIENTS: Eight patients with pseudomyxoma peritonei, five with mucinous tumors of the ovary and three with mucoceles of the appendix. INTERVENTION: All patients underwent cytoreductive surgery with removal of source i.e. panhysterectomy with appendicectomy in 5 and appendicectomy in 3. Systemic chemotherapy was used in 6 and systemic plus intraperitoneal chemotherapy in one case. RESULTS: Over 18 to 86 months' follow up, two patients died (at 18 and 24 mo) and 2 are alive with recurrence. Recurrence occurred only in those with inadequate clearance of mucinous material at the initial operation. The remaining 4 patients are free of disease. CONCLUSION: Aggressive surgical therapy with-chemotherapy is effective in providing long-term relief or cure in pseudomyxoma peritonei.