RESUMEN
Splanchnic vein thrombosis in patients with polycythemia rubra vera is well-known. Development of mobile right heart thrombus in these patients has not been reported previously. We describe a young patient with Polycythemia rubra vera and splanchnic vein thrombosis with ischemic bowel who underwent small bowel resection. He developed a large mobile right atrial thrombus and bilateral pulmonary embolism. He also had upper gastrointestinal bleed. His management was complicated and challenging due to multiple risk factors and co-morbid conditions. Thrombolysis was contraindicated and he refused surgical intervention. He was treated with anticoagulation with complete resolution of right atrial thrombus
Asunto(s)
Humanos , Masculino , Adulto , Trombosis , Embolia Pulmonar , Cardiopatías , Circulación Esplácnica , EcocardiografíaRESUMEN
Vascular ring is not an uncommon congenital anomaly. Since the opening of the cardiothoracic unit at the Royal hospital in December 1987, three children aged 4, 10 and 18 months with this anomaly were encountered. Their symptoms were stridor, recurrent respiratory tract infection and difficulty in swallowing = respectively. Barium swallow was the most reliable invastigation at arriving at a diagnosis. Digital subtraction angiography [DSA] was found to be helpful and less invasive than angiography to delineate the anatomy specially in small babies. Angiography was performed on the 18 months old boy to confirm the diagnosis. All three cases were of double aortic arch anomalies. Surgical repair was performed through left thoracotomy. There were no deaths and all patients were asymptomatic at the time of follow-up