Anesthesia in a child operated for cleft lip associated with Patau's syndrome / Anestesia em criança operada para lábio leporino associado à síndrome de Patau

Abstract Patients with Patau's syndrome (Trisomy 13) have multiple craniofacial, cardiac, neurological and renal anomalies with very less life expectancy. Among craniofacial anomalies cleft lip and palate are common. These craniofacial and cardiac anomalies present difficulties with anesthesia. We therefore describe the anesthetic management in the case of a Trisomy 13 child for operated for cleft lip at 10 months of age.

Resumo Os pacientes com síndrome de Patau (trissomia 13) apresentam várias anomalias craniofaciais, cardíacas, neurológicas e renais, com expectativa de vida bem menor. Entre as anomalias craniofaciais, o lábio leporino e a fenda palatina são comuns. Essas anomalias craniofaciais e cardíacas apresentam dificuldades na anestesia. Portanto, descrevemos o manejo anestésico em uma criança de 10 meses com trissomia 13 submetida à cirurgia de lábio leporino.

Calcifying Odontogenic Cyst of Mandible: A Case Report

The term calcifying odontogenic cyst was first introduced by Gorlin in 1962. It represents 2% of all odontogenic pathological changes in the jaw. The calcifying odontogenic cyst usually arises intraosseously, but it may also occur extraosseously, with about equal frequency in the mandible and maxilla (1:1). The age of the patients may range from 5 to 92 years, with peak incidence in the second and sixth decade of life. Radiographically, the lesion appears as a unilocular or multilocular well-defined radiolucency that may contain small irregular calcified bodies of varying sizes, and it may be associated with an odontome or an unerupted tooth. We present a case report of 17year-old female with Calcifying odontogenic cyst involving right body and angle of mandible.