RESUMEN
A giant retroperitoneal desmoid (30 x 15 cm), in a 16-year old girl arising from psoas fascia is reported. Despite debulking surgery, adjuvant radiotherapy, anti-oestrogen agents and non-steroidal anti-inflammatory agents, 3 years later she died from tumour invasion of major blood vessels and bowel, leading to massive gastrointestinal bleeding.
Asunto(s)
Adolescente , Femenino , Fibromatosis Agresiva/diagnóstico , Humanos , Neoplasias Retroperitoneales/diagnósticoAsunto(s)
Dolor Abdominal/diagnóstico , Adenoma/diagnóstico , Adulto , Biopsia con Aguja , Carcinoma de Células Renales/diagnóstico , Diagnóstico Diferencial , Humanos , Inmunohistoquímica , Neoplasias Renales/diagnóstico , Masculino , Nefrectomía , Tomografía Computarizada por Rayos X , Ultrasonografía DopplerRESUMEN
Leiomyoma of the urethra is a rare clinical entity. We report an unusual presentation of this tumour, which led to a diagnostic and surgical dilemma. The patient was a 16-year old female who presented with a labial mass which was palpable abdominally. Imaging methods and laparoscopy demonstrated a well defined soft tissue mass arising from the pelvis, without any obvious involvement of the urinary tract. The tumour (8 x 10 cm) was completely excised with reconstruction of the bladder and urethra. Histology confirmed a cellular leiomyoma.