RESUMEN
Based on the clinical data of a case of fibrocalculous pancreatic diabetes (FCPD) and literature review, we analyze the etiology, clinical manifestations, diagnostic criteria, treatment, and prognosis of the disease. FCPD is a unique form of diabetes mellitus secondary to pancreatic exocrine disease. The disease is restricted to adolescent or young adult of either sex with poor nutrition in tropical regions of the world. FCPD is characterized by simultaneous involvement of pancreatic endocrine and exocrine functions with clinical manifestations as pancreatic duct stones, pancreatic calcification, and diabetes mellitus. Treatment includes improved nutrition, blood glucose control, and pancreatic duct lithotomy. It could be easy to be misdiagnosed and mistreated, which deserves more attention from clinicians.