MR Images of Spontaneously Involuted Atretic Cephalocele Concomitant with Persistent Falcine Sinus in an Adult

Atretic cephalocelces are defined as skin-covered midline subscalp lesions that contain meninges and rest of glial and/or central nervous system tissue. When the straight sinus is absent or rudimentary, the falcine sinus can be recanalized to enable venous drainage. Although the atretic cephalocele or persistent falcine sinus has largely been described in the pediatric population, it is a rarely observed in the adult population. We report a unique case of spontaneously involuted atretic cephalocele coexistent with persistent falcine sinus in an adult. MR images and MR venography were useful for diagnosis and accurate anatomical depiction.

Atretic Cephalocele

We report a case of atretic cephaloce in a 7-month-old girl who presented with a growing left parietal painful mass, which was covered with excessive growth of thick scalp hairs and purplish discolored skin. Preoperative radiological studies revealed the left parietal round skull defect and epidural well enhancing mass without significant intradural parenchymal and vascular malformation. Total excision was done and histological diagnosis of atretic cephalocele was done. Characteristic histopathological features of this rare congenital anomaly with pertinent review of literatures were presented.

Atretic Cephalocele

We report a case of atretic cephaloce in a 7-month-old girl who presented with a growing left parietal painful mass, which was covered with excessive growth of thick scalp hairs and purplish discolored skin. Preoperative radiological studies revealed the left parietal round skull defect and epidural well enhancing mass without significant intradural parenchymal and vascular malformation. Total excision was done and histological diagnosis of atretic cephalocele was done. Characteristic histopathological features of this rare congenital anomaly with pertinent review of literatures were presented.