RESUMEN
Resumen Es una enfermedad poco frecuente, descripta en 1992 por Moulin, que se presenta entre los 6 y los 20 años de edad, caracterizada por bandas hiperpigmentadas atróficas de distribución blaschkoide, localizadas principalmente en tronco, unilaterales, que no son precedidas por inflamación o cambios esclerodérmicos, induración ni adherencias a planos profundos. En general es una afección autolimitada, cuyos tratamientos resultan ineficaces. Presentamos el caso de un niño de 12 años, con lesiones en tronco compatibles con el diagnóstico de Atrofodermia lineal de Moulin (ALM).
Abstract It is a disease not very frequent, described in 1992 by Moulin, which occurs between 6 and 20 years of age, characterized by hyperpigmented atrophic bands distribution blaschokoide, mainly located in trunk, unilateral, that are not preceded by inflammation or changes sclerodermal, induration, or adhesions to deep. It is a self-limited condition, whose treatments are ineffective. We present the case of a boy, 12 years old, with atrophic, hyperpigmented and asymptomatic plates, distributed from the left mammary region to the homolateral back, following the lines of Blaschko. Refers that is started as a hyperpigmented macula and in recent years it has been atrophying, it is not accompanied by any symptomatology, and was not preceded by inflammatory. We performed laboratory test with complete blood count, renal function, liver function and antibody titers, which were normal; and incisional biopsy by punch, that reported, for a sample stained with hematoxylin-eosin, epidermis of variable thickness, canned, no cellular atypia or disorders madurativos. Dermis impresses discreetly thickened, with homogenization of collagen. Slight perivascular inflammatory infiltrate. With clinical and anatomopathology we arrive at the diagnosis of Linear atrophoderma of Moulin.
RESUMEN
La atrofodermia lineal de Moulin es una patología poco frecuente que se presenta en niños sanos y adultos jóvenes. Se manifiesta con lesiones que siguen las líneas de Blaschko. Ocurre sin estar precedida de inflamación, induración, esclerodermia o atrofia epidérmica.Debemos hacer diagnóstico diferencial principalmente con atrofodermia idiopática de Pasini y Pierini y morfea. Tiene pronóstico favorable y no se la ha asociado a otras anomalías. Los tratamientos descritos han sido poco favorables. Presentamos el caso de unamujer de 15 años, con lesiones lineales en dorso y brazo, compatibles con atrofodermia lineal de Moulin.
The linear atrophoderma of Moulin is a rare disease that occurs in healthy children andyoung adults. It manifests with lesions along the lines of Blaschko. It occurs without precedinginflammation, induration, scleroderma or epidermal atrophy. Primarily, we shouldmake the differential diagnosis with idiopathic atrophoderma of Pasini and Pierini andmorphea. It has a favorable prognosis and it has not been associated with other anomalies.The treatments described have been unsuccessfull. We report a 15-year-old woman,with linear lesions on the back and arm compatible with linear atrophoderma of Moulin.