RESUMEN
Bronchogenic cysts( BC) is a congenital malformation of the lung which is common in chil-dren and adolescents. Because the disease is rare and not characteristic in symptom,sign and imaging,it can be easily misdiagnosed. It is still difficult to improve the rate of correct and early diagnosis. This article reviewes the research progress of the occurrence,symptom and management of BC.
RESUMEN
Objective To discuss the diagnosis and early intervention treatment of fetal congenital broncho-genic cysts based on the cases reviewed. Methods The clinical features of 7 infants presenting bronchogenic cysts diagnosed antenatally from January 2013 to May 2014 in Guangdong Women and Children's Hospital and Health In-stitute were reviewed retrospectively. Pathology,the prenatal diagnosis and treatment of bronchogenic cysts experience were summarized combined with CT after birth and surgery. Results Based on the prenatal diagnosis of fetal and postnatal CT and surgical pathology,a total of 7 cases with congenital bronchial cysts were diagnosed. Of which 4 ca-ses were suggestive of congenital cystsic adenomatoid malformation by prenatal diagnosis,and the other 3 cases had fetal bronchial cysts by prenatal diagnosis,antenatal diagnosis was accurate in 42. 9%(3 / 7 cases). CT examinations were taken in 7 cases after birth,and the cyst excision was performed on them with surgery thoracic approach;the average age at surgery was(5. 3 ± 1. 7)months. Four cases had simple bronchial cystss,2 cases with congenital cystsic adenomatoid malformation,1 case with congenital pulmonary sequestration. The accuracy of CT diagnosis was 85. 7%(6 / 7 cases). All surgical treatment was effective. Conclusions Fetal bronchial cysts is always associated with the other presence of lung congenital malformations. Prenatal diagnosis of congenital bronchial cysts is difficult. Prenatal diagnosis is difficult to exclude congenital cystsic adenomatoid malformation. To avoid symptoms like oppres-sion,infection,prenatal diagnosis combined with CT examination after birth and early treatment are necessary and reliable clinically.
RESUMEN
Cutaneous presentations of bronchogenic cysts are rare in all age groups, particularly in adults. Previous reports showed that cutaneous manifestations of bronchogenic cysts were frequently presented above abdominal region. Here we present two cases of a perianal bronchogenic cyst. To the best to our knowledge, this is the fi rst report of a bronchogenic cyst in this area.
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Bronchogenic cysts are usually located in the pulmonary parenchyma or in the mediastinum. When bronchogenic cysts are located in the mediastinum, they are usually near the bronchus or esophagus, and rarely located in the retroperitoneal space. It is difficult to differentiate between bronchogenic cysts and benign cysts prior to surgert. We report here on a patient for who had a mass in the retroperitoneum, with the preoperative diagnosis being a benign neurogenic tumor. Via left open thoracotomy, pathologic reports revealed that the mass was a bronchogenic cyst. We report here on the case of a bronchogenic cyst that was located in the retroperitoneal space of the diaphragm.
Asunto(s)
Humanos , Bronquios , Quiste Broncogénico , Diafragma , Esófago , Mediastino , Neoplasias Retroperitoneales , Espacio Retroperitoneal , ToracotomíaRESUMEN
Congenital cystic lung lesions are a group of congenital lung diseases with low incidence. These include congenital cystic adenomatoid malformation,bronchogenic cyst,congenital lobar emphysema and pulmonary sequestration. These malformations occur during the period of lung development stimulated by various factors. Manifestations of the diseases are very similar,but the pathogenesis and pathology are very different. Congenital cystic adenomatoid malformations are thought to be the results of the cessation of bronchiolar maturation with overgrowth of mesenchymal elements and without development of alveoli. There are 5 pathological types of congenital cystic adenomatoid malformations. Bronchogenic cysts are the results of abnormal budding from a segment of the tracheobronchial tree during embryo development,and the buds with no communication with normal tracheobronchial tree. Congenital lobar emphysema is a term reserved for hyperinflation of alveoli from idiopathic reasons or extrinsic compression,as well as pathological changes of the bronchial wall. Pulmonary sequestrations account for parts of nonfunctioning lung tissue that mostly do not communicate with normal bronchoalveolar tree and vascularized by a systemic artery,two types(intralobar and extralobar sequestration)are described.
RESUMEN
El quiste broncogénico es una malformación de la porción ventral del intestino primitivo que ocasiona alteración en el desarrollo del árbol traqueobronquial. Comunicamos dos casos de quistes broncogénicos que se acompañaron de síntomas respiratorios; uno, de localización mediastinal paratraqueal derecha y, el otro, intraparenquimatoso en lóbulo inferior derecho. La radiografía y tomografía de tórax permitieron evaluar la presencia, localización, tamaño y relación de los quistes con las vías aéreas. Ambos pacientes fueron operados sin complicaciones; los síntomas respiratorios desaparecieron. El estudio histopatológico confirmó el diagnóstico.
Bronchogenic cysts are malformations of the ventral portion of the primitive gut that cause an alteration in the development of the tracheobronchial tree. We report two cases of bronchogenic cysts with respiratory symptoms. A 32 year old woman had a mediastinal cyst at the right paratracheal level and the other was an eight month old boy with an intraparenchymal cyst in the right lower lobe. Chest X-rays and CA T scans are mandatory to determine the presence, exact location, size and relationships of the cysts to the larger airways. Both patients were resected without complications and have been asymptomatic. The histopathological study confirmed the diagnosis.