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Journal of Korean Medical Science ; : 824-828, 2011.
Artículo en Inglés | WPRIM | ID: wpr-58116

RESUMEN

Waldenstrom macroglobulinemia (WM) is a B-cell lymphoproliferative disorder associated with bone marrow involvement of lymphoplasmacytic lymphoma (LPL) and an IgM monoclonal gammopathy. Generally B-lymphocytes in LPL do not express CD5 that is important for differential diagnosis of B-cell lymphoproliferative disorders. In WM, various renal diseases and type I cryoglobulinemia are well described separately, but cryoglobulinemic glomerulonephropathy is very rarely reported. A 61-yr-old woman complained of generalized edema, cyanosis of the extremities in cold weather, visual disturbance, and pancytopenia. Bone marrow and renal biopsy showed CD5+ expressing B-cells and cryoglobulinemic glomerulonephropathy. With the diagnosis of WM, she received cyclophosphamide, doxorubicin, vincristine and prednisolone chemotherapy and got complete remission. Here, we report a rare case of WM associated with unusual expression of CD5+ B-lymphocytes and cryoglobulinemic glomerulonephropathy, and emphasize the importance of the clinical features in differentiating CD5+ B-cell lymphoproliferative disorders.


Asunto(s)
Femenino , Humanos , Persona de Mediana Edad , Antígenos CD5/metabolismo , Antineoplásicos/uso terapéutico , Linfocitos B/inmunología , Médula Ósea/patología , Crioglobulinemia/diagnóstico , Ciclofosfamida/uso terapéutico , Diagnóstico Diferencial , Doxorrubicina/uso terapéutico , Quimioterapia Combinada , Glomerulonefritis/diagnóstico , Riñón/patología , Paraproteinemias/diagnóstico , Prednisolona/uso terapéutico , Vincristina/uso terapéutico , Macroglobulinemia de Waldenström/diagnóstico
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