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Indian J Dermatol Venereol Leprol ; 2013 Nov-Dec; 79(6): 802-804
Artículo en Inglés | IMSEAR | ID: sea-154686

RESUMEN

Dowling Degos disease is a rare, reticulate pigmentary disorder with variable phenotypic expression that manifests as hyperpigmented macules and reticulate pigmentary anomaly of the fl exures. Many variants of this condition and its overlap with other reticulate pigmentary disorders have been reported in the literature. We present here two cases of DDD with follicular localization, both clinically and histologically. It was associated with ichthyosis vulgaris in one case. Follicular DDD is an uncommon variant of this evolving dermatosis. Our report supports the possible role for disordered follicular keratinisation in its pathogenesis.


Asunto(s)
Adulto , Femenino , Humanos , Hiperpigmentación/diagnóstico , Hiperpigmentación/terapia , Masculino , Enfermedades de la Piel/diagnóstico , Enfermedades de la Piel/terapia , Enfermedades Cutáneas Genéticas/diagnóstico , Enfermedades Cutáneas Genéticas/terapia , Enfermedades Cutáneas Papuloescamosas/diagnóstico , Enfermedades Cutáneas Papuloescamosas/terapia , Adulto Joven
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