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1.
Rev. chil. pediatr ; 91(3): 405-409, jun. 2020. tab, graf
Artículo en Español | LILACS | ID: biblio-1126179

RESUMEN

Resumen: Introducción: La Hidradenitis palmoplantar ecrina idiopática (HPPI) es una dermatosis neutrofílica infrecuente, que cursa con nódulos eritematosos dolorosos de comienzo brusco en regiones plantares o palmoplantares, en niños que no tienen otra enfermedad subyacente. Objetivo: Presentar un caso que ilustra las principales características clínicas e histológicas de la HPPI. Caso Clínico: Niña de 11 años evaluada por nódulos eritematovioláceos dolorosos en planta de pie derecho de 48 horas de evo lución y fiebre de hasta 38,2 °C, sin antecedentes de interés salvo hiperhidrosis y práctica intensa de ejercicio en los días previos. Ante la sospecha clínica de HPPI se realizó biopsia cutánea, que mostró infiltrado inflamatorio neutrofílico alrededor de glándulas sudoríparas ecrinas y abscesos de neutrófilos, confirmando el diagnóstico. Se indicaron antiinflamatorios no esteroidales orales y reposo, con resolución de las lesiones en 7 días. Conclusiones: Este caso demuestra los aspectos más importantes de la HPPI. Esta entidad en muchos casos es infradiagnosticada, dado que puede confundirse con otras patologías que también cursan con nódulos acrales dolorosos, pero tienen distintas implicacio nes patogénicas y terapéuticas. Identificar apropiadamente la HPPI permite evitar la alarma innece saria, tanto en pacientes y sus padres, como en los propios dermatólogos y pediatras.


Abstract: Introduction: Idiopathic Palmoplantar Eccrine Hidradenitis (IPPH) is a rare neutrophilic derma tosis, with painful erythematous nodules of sudden onset in the plantar or palmoplantar region, in children without other underlying diseases. Objective: To present a case that shows the main clinical and histological characteristics of this entity. Clinical Case: 11-year-old girl with a 48-hours history of painful erythematous-violaceous nodules on the right foot plant associated with fever of up to 38.2 °C, with no history of interest except hyperhidrosis and intense exercising on previous days. Given the clinical suspicion of IPPH, a skin biopsy was performed, which showed inflammatory neutrophil infiltration around eccrine sweat glands and neutrophilic abscesses, confirming the diagnosis. Oral NSAIDs and rest were prescribed, with resolution of the lesions in 7 days. Conclusions: This case demonstrates the most important aspects of this entity, in many cases underdiagnosed, since it can be confused with other pathologies that occur with painful acral nodules, but have different pathogenic and therapeutic implications. To properly identify the IPPH allows preventing an unnecessary alarm, both patients and their parents, as in dermatologists and pediatricians themselves.


Asunto(s)
Humanos , Femenino , Niño , Hidradenitis/diagnóstico , Dermatosis del Pie/diagnóstico , Hidradenitis/complicaciones , Hidradenitis/patología , Dolor Agudo/etiología , Dermatosis del Pie/complicaciones , Dermatosis del Pie/patología
2.
An. bras. dermatol ; 90(3,supl.1): 175-177, May-June 2015. ilus
Artículo en Inglés | LILACS | ID: lil-755772

RESUMEN

Abstract

Palmoplantar lichen planus is an uncommon dermatosis. We present a case of 38-year-old Caucasian male with a history of pruritic, scaly lesions on the right plantar foot. Physical examination revealed whitish plaques and numerous spiny hyperkeratotic papules and focal scaling. A biopsy demonstrated orthohyperkeratosis and acanthosis of the epidermis. Immunohistochemical staining revealed positivity within the epidermis and/or lichenoid infiltrate with CD3, CD8, CD45, CD68, myeloid histiod antigen, BCL2, p27, p53, HLA-DPDQDR, metallothionein and tissue inhibitor of metalloproteinases 1. The diagnosis of PPLP was thus confirmed; this case illustrates that PPLP should be considered in the differential diagnosis of uncommon foot dermatoses with a significant junctional inflammatory component.

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Asunto(s)
Adulto , Humanos , Masculino , Dermatosis del Pie/patología , Dermatosis de la Mano/patología , Liquen Plano/patología , Biopsia , Diagnóstico Diferencial , Epidermis/patología , Inmunohistoquímica
3.
Rev. méd. Chile ; 140(12): 1585-1588, dic. 2012. ilus
Artículo en Español | LILACS | ID: lil-674031

RESUMEN

We report a 66-year-old male presenting with malaise, heartburn and pruritic seborrheic keratoses in both feet of sudden onset, suggesting a Leser-Trélat sign. An upper gastrointestinal endoscopy disclosed a gastric cancer. The patient was subjected to a total gastrectomy and duringfollow up, the skin lesions had disappeared.


Asunto(s)
Anciano , Humanos , Masculino , Adenocarcinoma/complicaciones , Enfermedades del Pie/complicaciones , Queratosis Seborreica/complicaciones , Síndromes Paraneoplásicos/complicaciones , Neoplasias Gástricas/complicaciones , Enfermedades del Pie/patología , Queratosis Seborreica/patología , Síndromes Paraneoplásicos/patología
4.
An. bras. dermatol ; 86(6): 1222-1223, nov.-dez. 2011. ilus
Artículo en Portugués | LILACS | ID: lil-610436

RESUMEN

A acroceratoelastoidose é um tipo de ceratodermia palmoplantar, originalmente descrita pelo dermatologista mineiro Oswaldo Gonçalves Costa. É uma rara genodermatose autossômica dominante, embora possa ocorrer de forma esporádica. A doença não é congênita, com as primeiras manifestações na infância e adolescência. O quadro clínico é caracterizado por múltiplas pápulas amareladas, por vezes translúcidas e ceratóticas, medindo aproximadamente 2-4 mm de diâmetro, ocasionalmente umbilicadas, localizadas na margem lateral das mãos e pés, simetricamente, o que é sua expressão clínica mais típica. Os achados histopatológicos mais comuns são: hiperceratose, acantose discreta e elastorrexe, que é observada pela coloração com orceína.


Acrokeratoelastoidosis is a type of palmoplantar keratoderma first described by Oswaldo Gonçalves Costa, a Brazilian Dermatologist from the state of Minas Gerais. It is a rare autosomal-dominant genodermatosis; however it may occur sporadically. The disease is not congenital; rather, its onset occurs in childhood or adolescence. Clinically, the condition is characterized by multiple yellowish papules, sometimes glossy and keratotic, measuring approximately 2-4 mm in diameter, sometimes umbilicated, and located symmetrically on the sides of the hands and feet, symmetry being the most typical sign. The most common histopathological findings are hyperkeratosis, mild acanthosis and elastorrhexis, as revealed by orcein staining.


Asunto(s)
Adulto , Humanos , Masculino , Carcinoma de Células Escamosas/patología , Úlcera de la Pierna/patología , Neoplasias Cutáneas/patología
5.
An. bras. dermatol ; 84(5): 550-552, set.-out. 2009. tab
Artículo en Portugués | LILACS | ID: lil-535327

RESUMEN

Atletas apresentam risco para micoses cutâneas. Estudados 23 jogadores de futebol, através de exames clínico, micológicos (direto e cultura) e clipping ungueal, dezoito (78,26 por cento) não apresentavam micoses; dois (8,70 por cento) apresentavam tinea pedis e três (13,04 por cento) onicomicose, associada à tinea pedis, principalmente por Trichophyton mentagrophytes. Tinea pedis infectada produziu celulite em um atleta. É necessário um programa educativo de cuidados com a pele no esporte.


Athletes present risk of cutaneous mycosis. A study was carried out with 23 soccer players using clinical and mycological examination (direct microscopic examination and culture) and nail clipping. Eighteen (78.26 percent) did not present mycosis; two (8.70 percent) presented tinea pedis, and three (13.04 percent) presented onychomycosis associated to tinea pedis, mainly for Trichophyton mentagrophytes. Infected tinea pedis has produced cellulitis in one of the athletes. It is necessary to create an educative program of skin care during sports practice.


Asunto(s)
Adolescente , Adulto , Humanos , Adulto Joven , Onicomicosis , Fútbol , Tiña del Pie , Estudios Transversales , Onicomicosis/diagnóstico , Onicomicosis/epidemiología , Tiña del Pie/diagnóstico , Tiña del Pie/epidemiología , Adulto Joven
6.
An. bras. dermatol ; 83(5): 441-443, set.-out. 2008. ilus
Artículo en Portugués | LILACS | ID: lil-502782

RESUMEN

Hiperceratose focal acral é dermatose rara caracterizada por pápulas ceratóticas acrais que afetam preferencialmente as superfícies marginais das mãos e dos pés, pertencendo ao grupo das hiperceratoses marginais. Apresentamos variante inédita de mulher de 45 anos de idade, branca, dona-de-casa, sem história familiar, com lesões ceratóticas papulosas localizadas nos pés e hipocromia de dermatóglifos na região afetada. Histologicamente apresentou hiperortoceratose, desnível da epiderme (degrau), acantose e hipergranulose. Os tratamentos com ceratolíticos tópicos foram ineficientes, de forma semelhante aos casos descritos na literatura atual.


Focal acral hyperkeratosis is a rare condition, characterized by acral keratotic papules that preferably affect hand and foot surfaces, and are included in the spectrum of marginal papular keratodermas. We report an unpublished variant of this condition, the case of a 45-year-old Caucasian woman with acral keratotic papular lesions and hypochromic dermatoglyphics in the feet. Histological examination revealed orthohyperkeratosis, depression of the epidermis, acanthosis and hypergranulosis. Topical treatments with keratolytics were ineffective, similarly to previously described cases.

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