Central Cemento-Ossifying Fibroma: Clinical Imaging and Histopathological Diagnosis / Fibroma Cemento-Osificante Central: Diagnóstico Clínico, Imagenológico e Histológico

ABSTRACT: Central ossifying fibroma is a lesion in which diagnosis has proved intriguing and unclear for presenting clinical, radiographic, and even histopathological similarities to other types of lesions such as the fibrous dysplasia of bone and cement-bone dysplasia. It is a benign neoplasm of uncertain etiology and slow development in which the mandible is affected more frequently than the maxilla. We described a case of central cemento-ossifying fibroma involving the right mandible of a thirty-five-female patient by presenting its clinical, radiographic, and histological characteristic sand discussing some differential diagnoses.

RESUMEN: El fibroma cemento-osificante central es una lesión que requiere un diagnóstico diferencial ya que muestran similitud clínica, histológica y radiológica con la displasia fibrosa y con la displasia cemento-ósea. Esta lesión es un tumor benigno de etiología incierta, presenta crecimiento lento y afecta principalmente la mandíbula más que el maxilar. Se reporta un caso de un paciente de sexo femenino de 35 años, diagnosticada con fibroma cementoosificante central que le afectó el lado derecho de la mandíbula. Se describen las características clínicas, histológicas y radiológicas de la paciente y se discuten los diversos diagnósticos diferenciales.

Nonsurgical treatment for a severe anterior and lateral open bite and multiple congenitally missing teeth: a case report with 4-year follow-up

ABSTRACT This case report describes the treatment of a severe anterior and lateral open bite combined with multiple congenitally missing teeth. A 10-year-old girl presented with an open gonial angle, absence of lip sealing, and soft tissue pogonion retrusion. She had an open bite of 8.5 mm, agenesis of the upper right and left lateral incisors and the upper left first premolar, and transverse maxillary deficiency. Nonsurgical treatment was planned aiming at controlling the vertical pattern, establishing the correct overbite, and closing the spaces on the upper arch, to provide satisfactory occlusion and facial and dental esthetics.

RESUMO O presente caso clínico descreve o tratamento de uma mordida aberta anterior e lateral associada à ausência congênita de dentes permanentes. Paciente com 10 anos de idade, apresentava ângulo goníaco aberto, ausência de selamento labial passivo e retrusão do pogônio mole. Além disso, foi diagnosticada uma mordida aberta de 8,5 mm, agenesia de incisivos laterais superiores direito e esquerdo e de primeiro pré-molar superior esquerdo, além de deficiência transversa da maxila. O planejamento do caso envolveu um tratamento não cirúrgico, com controle vertical do crescimento, obtenção de correta sobremordida e fechamento dos espaços superiores. O caso foi finalizado com uma boa intercuspidação, contemplando a estética facial e dentária.

Florid cemento-osseous dysplasia and peripheral giant cell granuloma in a patient with neurofibromatosis 1

Abstract: We report a 35-year-old mulatto female patient with neurofibromatosis Type 1 who presented with facial asymmetry. The patient had two lesions: florid cemento-osseous dysplasia associated with peripheral giant cell granuloma. She was referred for surgical treatment of the peripheral giant cell granuloma and the florid cemento-osseous dysplasia was treated conservatively by a multidisciplinary team. So far, no changes have been observed in the patient's clinical status. We observed no recurrence of peripheral giant cell granuloma. To the best of our knowledge, the present case is the first report of a patient with neurofibromatosis Type 1 associated with a giant cell lesion and florid cemento-osseous dysplasia.

Alteraciones estéticas faciales en el síndrome de seno silente / Facial aesthetic alterations in silent sinus syndrome / Alterações estéticas faciais na síndrome do seio silencioso

Introducción: el Síndrome de Seno Silente (SSS) es una entidad rara, siendo poco frecuente el hundimiento del maxilar superior como motivo de consulta. El trabajo pretende realizar una revisión de la bibliografía del SSS con el hundimiento del maxilar superior como principal manifestación. Material y método: Se realizó una revisión bibliográfica de artículos publicados desde el año 2008 a la actualidad. Se revisaron las historias clínicas de los pacientes diagnosticados con SSS, intervenidos quirúrgicamente. Como criterios diagnósticos se tuvieron en cuenta: asimetría facial, ausencia de síntomas rinosinusales, tomografía de macizo cráneo facial (TC MCF) con velamiento del seno maxilar y disminución de su volumen, y aumento del volumen orbitario. Se evaluó el seguimiento postoperatorio y sus resultados. Resultados: El SSS se debe a un proceso inflamatorio en el seno maxilar que genera aumento de las presiones negativas. Clínicamente se caracteriza por asimetría facial. El diagnóstico se confirma por tomografía, siendo lo más característico la presencia, en el plano coronal, de un seno maxilar ocupado y atelectásico y el descenso del piso orbitario con disminución del volumen del mismo y aumento del volumen de la órbita. El tratamiento quirúrgico se basa en mejorar las presiones dentro del seno maxilar, reservando el tratamiento del piso de la órbita a aquellos pacientes en los que persisten las alteraciones estéticas. Conclusiones: La asimetría facial es el principal motivo de consulta del paciente. Sin embargo el hundimiento del seno maxilar no es la causa más frecuente de asimetría.

Introduction: silent Sinus Syndrome (SSS) is a rare entity, and the subsidence of the upper jaw is rare. The paper aims to review the SSS literature with the upper jaw collapse as the main manifestation. Material and method: A bibliographic review of articles published from the year 2008 to the present time was carried out. Were viewed the medical records of patients diagnosed with SSS, whounder went surgery. As diagnostic criteria were taken into account: facial asymmetry, absence of rhinosinusal symptoms, massive facial cranial tomography with maxillary sinus veil and diminished volume, and increased orbital volume. Postoperative follow-up and results were evaluated. Results: The SSS is due to an inflammatory process in the maxillary sinus that generates an increase of the negative pressures. Clinically it is characterized by facial asymmetry. The diagnosis is confirmed by tomography being the most characteristic the presence, in the coronal plane, of a occupied maxillary sinus and atelectatic and the descent of the orbital floor with decrease of the volume of the same and increase of the volume of the orbit. The surgical treatment is based on improving the pressure inside the maxillary sinus, reserving the treatment of the floor of the orbit to those patients who persist the aesthetic alterations. Conclusions: Facial asymmetry is the main reason for patient consultation. However, sagging of the maxillary sinus is not the most frequent cause of asymmetry.

Introdução: síndrome do Sinus Silencioso (SSS) é uma entidade rara, e o maxilar inferior não é freqüente como motivo de consulta. O artigo pretende rever a literatura SSS com o colapso do maxilar superior como principal manifestação. Material e método: Foi realizada uma revisão bibliográfica de artigos publicados de 2008 para o presente. Revisamos os registros médicos de pacientes diagnosticados com SSS, que foram submetidos a cirurgia. Como critérios de diagnóstico foram tidos em conta: assimetria facial, ausência de sintomas rinossinusais, tomografia craniana facial maciça com velamento maxilar superior e volume diminuído e aumento do volume orbital. O acompanhamento pós-operatório e os resultados foram avaliados. Resultados: SSS é devido a um processo inflamató- rio no seio maxilar que gera um aumento nas pressões negativas. Clinicamente, é caracterizada por assimetria facial. O diagnóstico é confirmado pela tomografia sendo a mais característica a presença, no plano coronal, de um seio maxilar ocupado e atelectásico e a descida do piso orbital com diminuição do volume do mesmo e aumento do volume da órbita. O tratamento cirúrgico baseia-se na melhoria da pressão dentro do seio maxilar, reservando o tratamento do piso da órbita aos pacientes que persistem as alterações estéticas. Conclusões: A assimetria facial é o principal motivo para a consulta do paciente. No entanto, a flacidez do seio maxilar não é a causa mais frequente de assimetria.

Surgical Treatment of Condylar Hyperplasia Associated with Dentofacial Deformity: Low Condylectomy, Articular Disc Repositioning, and Orthognathic Surgery / Tratamiento Quirúrgico de Hiperplasia Condilar Asociado a la Deformidad Dentofacial: Condilectomía Baja, Reposicionamiento del Disco Articular y Cirugía Ortognática

Due to the complexity of the treatment of condylar hyperplasia associated with dentofacial deformities and its complications, if left untreated, the surgeon should be alert to these factors at the time of surgical planning to tailor the optimal therapy for an individual patient. This case report describes a patient with right condylar hyperplasia associated with dentofacial deformity who was treated surgically with low condylectomy, articular disc repositioning and anchoring, and orthognathic surgery, concomitantly, with stable results, satisfactory occlusion and facial harmony.

Debido a la complejidad del tratamiento de la hiperplasia condilar asociada con deformidades dentofaciales y sus complicaciones, si no se trata, el cirujano debe estar alerta ante estos factores en el momento de la planificación quirúrgica para adaptar la terapia óptima para cada paciente. Este caso describe un paciente con hiperplasia condilar derecha asociada con la deformidad dentofacial que fue tratado quirúrgicamente con condilectomía baja, reposicionamiento y anclaje del disco articular, y la cirugía ortognática, concomitantemente, con resultados estables, oclusión satisfactoria y armonía facial.

La artritis reumatoidea juvenil y su influencia en la alteración de desarrollo de la mandíbula / Juvenile rheumatoid arthritis and its influence on the alteration of jaw development

La artritis reumatoidea juvenil (ARJ) es una enfermedad inflamatoria autoinmune que se presenta en niños menores de 16 años. Es de curso crónico, etiología desconocida, y afecta sobre todo las articulaciones, como la temporomandibular (ATM). El daño de la ATM puede ocasionar: alteraciones en el crecimiento facial (micrognatia), maloclusión clase II, mordida abierta anterior, desviaciones laterales, erosiones óseas, destrucción del cón-dilo, oclusión disfuncional y alteración de la estética facial, entre otras consecuencias. La posición oclusal neurofisiológica lograda por medio de elementos electrónicos, como el Transcutaneus Electrical Neural Stimulation (TENS), y mantenida por el Dispositivo Intaroral (DIO) podría posibilitar la remodelación de la cabeza del cóndilo, en pacientes en crecimiento, en los que la enfermedad se halla controlada, regulando así también la sintomatología dolorosa...

Facial asymmetry: a current review

Abstract The term "asymmetry" is used to make reference to dissimilarity between homologous elements, altering the balance between structures. Facial asymmetry is common in the overall population and is often presented subclinically. Nevertheless, on occasion, significant facial asymmetry results not only in functional, but also esthetic issues. Under these conditions, its etiology should be carefully investigated in order to achieve an adequate treatment plan. Facial asymmetry assessment comprises patient's first interview, extra- as well as intraoral clinical examination, and supplementary imaging examination. Subsequent asymmetry treatment depends on patient's age, the etiology of the condition and on the degree of disharmony, and might include from asymmetrical orthodontic mechanics to orthognathic surgery. Thus, the present study aims at addressing important aspects to be considered by the orthodontist reaching an accurate diagnosis and treatment plan of facial asymmetry, in addition to reporting treatment of some patients carriers of such challenging disharmony.

Resumo O termo assimetria é utilizado quando existe uma desigualdade entre as partes homólogas, afetando, assim, o equilíbrio entre as estruturas. A assimetria facial é comum na população, e muitas vezes se apresenta de forma subclínica. Entretanto, em alguns casos existe uma assimetria facial significativa que resulta tanto em problemas funcionais quanto estéticos. Nessas circunstâncias, a etiologia deve ser cuidadosamente investigada, para que seja possível elaborar um plano de tratamento adequado. A avaliação da assimetria facial é constituída por uma anamnese do paciente, exame clínico extra e intrabucal, além de exames complementares de imagem. O tratamento subsequente dessa assimetria depende da idade do paciente, etiologia e da magnitude da desarmonia, podendo envolver desde mecânicas ortodônticas assimétricas até a realização de cirurgia ortognática. Assim, o presente artigo busca abordar aspectos importantes para que o ortodontista possa realizar um adequado diagnóstico e plano de tratamento da assimetria facial, além de relatar o tratamento de alguns pacientes portadores dessa desafiadora desarmonia.

Orthodontic-surgical management of a case of severe mandibular deficiency due to condylar ankylosis.

Dentofacial deformities involve deviations from the normal facial proportions and dental relationships and can range from mild to being severe enough to be severely handicapping.The term handicapping malocclusions though not a term commonly used, involves a fortunately small section (2-4%) of patients who can suffer from esthetic,psychological and functional problems. Craniofacial Orthodontics is the area of orthodontics that treats patients with congenital and acquired deformities of the integument and it's underlying musculoskeletal system within the craniofacial area and associated structures.This case report of a young woman with severe mandibular deficiency and facial asymmetry due to condylar ankylosis highlights the importance of team work in rehabilitation of such severe craniofacial deformities

Alterações da articulação temporomandibular e suas repercussões orofaciais em pacientes portadores de artrite idiopática juvenil / Temporomandibular joint alterations and their orofacial complications in patients with juvenile idiopathic arthritis

Os pacientes com artrite idiopática juvenil (AIJ) podem apresentar alterações no metabolismo ósseo e no crescimento esqueletal, além de danos na articulação temporomandibular (ATM), o que pode gerar alterações extraorais e/ou intraorais, acarretando distúrbios craniofaciais. Nosso objetivo é promover uma revisão da literatura sobre as alterações orofaciais em pacientes com AIJ. Dentre os distúrbios orofaciais em pacientes com AIJ, as mudanças no crescimento mandibular, geradas por disfunções na região da ATM, parecem de grande prevalência nesses pacientes. As alterações mais encontradas são: retrognatismo, micrognatia, mordida aberta anterior, apinhamento dentário, assimetria facial e limitação de abertura de boca. Assim, o reumatologista torna-se uma peça-chave na detecção precoce dessas disfunções, ajudando no encaminhamento do paciente ao dentista. O diagnóstico, por sua vez, deve ser realizado pelo ortodontista, utilizando exames clínico e de imagem, o que possibilita tratamento precoce e prognóstico favorável. Distúrbios na ATM devem ser tratados de forma multidisciplinar, incluindo tratamento farmacológico para o controle da dor e tratamento odontológico por meio de aparelhagem funcional e/ou ortodôntica, fisioterapêutico e por vezes fonoaudiológico. Concluímos que dentre os distúrbios orofaciais em pacientes com AIJ, as mudanças no crescimento mandibular geradas por disfunções na região da ATM parecem de grande prevalência. Tais disfunções podem promover, principalmente, mordida aberta, retrusão mandibular, micrognatia, apinhamento dentário e assimetria facial. O reumatologista pode detectar tais alterações precocemente, encaminhando o paciente de imediato a uma equipe que deve ser, preferencialmente, multidisciplinar, composta por ortodontista, fisioterapeuta e fonoaudiólogo, visando reduzir futuras complicações oclusais e de crescimento mandibular.

Patients with juvenile idiopathic arthritis (JIA) can have alterations in bone metabolism and skeletal growth, as well as damage to the temporomandibular joint (TMJ), which can generate extra and/or intraoral alterations, resulting in craniofacial disorders. Our goal is to carry out a review of the literature on orofacial alterations in patients with JIA. Among the orofacial disorders in patients with JIA, alterations in mandibular growth, caused by dysfunctions in the TMJ region, seem highly prevalent in these patients. The most often found alterations are: retrognathia, micrognathia, anterior open bite, dental crowding, facial asymmetry and mouth opening limitation. Thus, the rheumatologist becomes a key agent in the early detection of these disorders, helping with patient referral to a dentist. The diagnosis, in turn, should be performed by the orthodontist, using clinical examination and imaging methods, allowing early treatment and a favorable prognosis. TMJ disorders should be treated by a multidisciplinary team, including pharmacological treatment for pain control and dental care through functional appliance and/or orthodontic therapy, physical therapy and sometimes, speech therapy. We conclude that among the orofacial disorders in patients with JIA, alterations in mandibular growth generated by dysfunctions in the TMJ region seem highly prevalent. Such dysfunctions can cause mainly open bite, mandibular retrusion, micrognathia, dental crowding and facial asymmetry. The rheumatologist can detect these alterations at an early stage, with immediate patient referral to a team that should preferably be a multidisciplinary one, consisting of an orthodontist, physical therapist and speech therapist, to reduce future occlusal and mandibular growth complications.

Masticación viciosa: diagnóstico radiográfico / Vicious chewing: radiographic diagnosis

La masticación es una función del sistema estomatognático fundamental para el desarrollo del tercio inferior y medio de la cara. Las alteraciones en el ciclo masticatorio durante el período de crecimiento y desarrollo podría traer aparejado problemas de asimetría facial. Las radiografías extraorales, telerradiografía y panorámica, son de gran utilidad en odontología. La Rx panorámica demostró ser un auxiliar de la clínica para el diagnóstico de la función masticatoria. La Dra. Wilma Simoes propuso un análisis de la Rx panorámica denominado panorograma de simetría. Este consiste en reunir información detallada de las estructuras de ambas mitades en la radiografía panorámica (derecha e izquierda) y compararlas entre sí, con el fin de reconocer las simetrías o asimetrías de las estructuras delt ercio medio e inferior de la cara.

Deformidad facial asimétrica: papel de la hiperplasia condilar / Asymmetric facial deformity: role of condylar hyperplasia

Las deformidades dentofaciales (DDF) son conocidas y su diagnostico es cada vez mas frecuente; las DDF asimétricas son un grupo de enfermedades de complejo manejo debido a las condicionantes estéticas y funcionales comprometidas. La etiología es variada, aunque la hiperplasia condilar suele estar asociada en los pacientes adolescentes y adultos; su diagnostico se establece mediante análisis facial, estudio con medicina nuclear, tomografías computadorizadas y otros exámenes. La terapéutica mas aceptada hoy día consiste en la condilectomia parcial y la corrección de la deformidad facial basada en las necesidades estéticas y funcionales del paciente. El objetivo de esta revisión es determinar las condicionantes actuales asociadas al diagnostico y tratamiento de las DDF asimétricas y el papel que cumple la hiperplasia condilar en el desarrollo de estas alteraciones faciales...

Dentofacial deformities (DDF) are know and the diagnosis is ever more executed; the asymmetric DDF are a group of disease with difficult management because of esthetic a functional conditions. The etiology is these conditions is varied, although the condylar hyperplasia is frequently in adolescent and adult patients; the diagnosis is realized by facial analysis, nuclear medicine study and computed tomography and others. The more accepted therapy is related to partial condilectomy and facial deformity correction in relation to aesthetic and functional needs of patient. The aim of this review is to determine the current conditions associated to diagnosis and treatment of asymmetric DDF and the role of condylar hyperplasia in the development of these facial alterations...

Goldenhar syndrome: clinical features with orofacial emphasis

OBJECTIVES: Goldenhar syndrome (GS) is a relatively common developmental disorder characterized by craniofacial anomalies in association with vertebral, cardiac, renal, and central nervous system defects. This paper describes GS features with special emphasis on oral characteristics. MATERIAL AND METHODS: The clinical features of 6 patients with GS aged 3 months to 12 years are described, and a brief review of the literature about this genetic disorder is presented. RESULTS: All patients demonstrated the classical triad of GS, including mandibular hypoplasia resulting in facial asymmetry, ear and/or eye malformation, and vertebral anomalies. In addition, renal and gastrointestinal abnormalities were observed in 2 patients. Regarding the oral involvement, 2 patients presented cleft lip and palate, and 1 patient had temporomandibular joint malformation. Malocclusion was found in all patients. CONCLUSION: Our orofacial findings correlate with the reported cases in the literature, and point out that after diagnosis GS patients need to be examined for systemic abnormalities.

Assimentria facial em indivíduos com mordida cruzada posterior por meio de fotografias / Facial asymmetry of individuals with posterior cross bite by means of photographs

Objetivo: Analisar a assimetria facial em indivíduos com mordida cruzada posterior, por meio de fotografias frontais e comparar os ângulos dos olhos e da boca com o plano mediano da face, verificando se estes ângulos são influenciados pela assimetria. Métodos: Foram avaliados 41 indivíduos. Realizaram-se fotografias frontais a fim de verificar se havia diferença a partir de traçados do plano dos olhos inter-pupilar e do plano da boca (linha da comissura), e mensurar estes ângulos em relação à linha média facial. Resultados: Quanto à análise frontal de fotografias, verificou-se que os dados relativos ao ângulo do olho não apresentaram diferenças estatisticamente significantes (p=0,6636) entre os lados direito e esquerdo, bem como o ângulo da boca (p=0,9460). Conclusão: O desvio funcional da mandíbula não promoveu alterações significativas na análise da face quando analisado os ângulos referentes à distância dos olhos e da boca em relação à linha média da face.

Objective: To analyze facial asymmetry of individuals with posterior cross bite by means of frontal photographs and compare the angles of eyes and mouth with the median plane of the face, to verify whether these angles are influenced by the asymmetry. Methods: Forty-one individuals were assessed. Frontal photographs were taken to verify whether there was a difference from the tracing of the interpupillary plane of the eyes and plane of the mouth (commissural line) and measure these angles in relation to the facial midline. Results: With regard to the frontal analysis of the photographs, it was verified that the data related to the angle of the eye showed no statistically significant differences (p=0.6636) between the right and left sides and the angle of the mouth (p=0.9460). Conclusion: Functional deviation of the mandible did not cause significant alterations in the analysis of the face when the angles with reference to the distance of the eyes and mouth in relation to the facial midline were analyzed.

Tratamiento de la deformidad facial causada por la hiperplasia condilar: relato de caso / Treatment of facial deformity caused by condylar hyperplasia: case report

La hiperplasia condilar es una anomalía de desarrollo adquirida, rara, caracterizada por el crecimiento excesivo y progresivo, afectando el cuello, la cabeza condilar, el cuerpo y la rama mandibular, provocando importante asimetría facial. En el artículo, se presenta un caso clínico de paciente del género masculino, 22 años de edad, quejándose de sintomatología dolorosa en la región de la articulación temporomandibular y asimetría facial severa. Fue instituido un tratamiento ortodóntico- quirúrgico por medio de cirugía ortognática combinada y condilectomía alta. Después de seis años de control postoperatorio, el paciente se presenta en buen estado, sin recidiva de la asimetría facial o de la hiperplasia condilar

The condylar hyperplasia is an acquired development anomaly, rare, characterized by an excessive and progressive growing, affecting neck, condilar head, body and the mandible bough, provoking an important facial asymmetry. In the article we present a case of male patient, 22-years-old, reclaiming of painful sintomatology in the region of temporomandibular joint and severe facial asymmetry. It was instituted an orthodontic-surgical treatment by means of orthognathic combined surgery and high condilectomy. After six years of post-surgical controlling, the patient is now in a good shape, without recurrence of facial asymmetry and condylar hyperplasia

Osteochondroma of the temporomandibular joint: a case report

Osteochondroma of the mandibular condyle has been found in the oral and maxillofacial region rarely. This paper describes a case of osteochondroma of the mandibular condyle in a 20-year-old woman, who was referred to our service with facial asymmetry, prognathic deviation of chin, cross-bite to the contralateral side, changes in condylar morphology, limited mouth opening, and malocclusion. Computed tomography (CT) was performed for better evaluation to the pathological conditions on the temporomandibular joint. Based on the clinical examination, patient history, and complementary exams, the hypothesis of osteochondroma was established. Condylectomy was performed using a preauricular approach with total removal of the lesion. After 3 years of postoperative follow up and orthodontic therapy, the patient is symptom-free, and has normal mouth opening with no deviation in the opening pattern.

Osteocondroma de côndilo mandibular é raro na região craniofacial. Este artigo descreve um caso de osteocondroma de côndilo mandibular em uma mulher de 20 anos que foi encaminhada ao nosso serviço apresentando assimetria facial, desvio de mento, mordida cruzada para o lado contralateral, alterações na morfologia condilar, limitação de abertura bucal e maloclusão. Tomografia computadorizada foi realizada para melhor avaliação da condição patológica da ATM. Devido à base no exame clínico, histórico do paciente e exames complementares, foi estabelecida uma hipótese de osteocondroma. Um procedimento de condilectomia utilizando abordagem preauricular com uma total remoção da lesão foi executado. Após três anos de acompanhamento pós-operatório e ortodôntico, o paciente está livre dos sintomas e tem uma abertura normal sem desvio de padrão durante a abertura.

Hipoplasia focal ectodérmica o síndrome de Goltz: manejo ortopédico témporomandibular / Focal dermal hypoplasia or Goltz síndrome: temporomandibular orthopedic management

El desarrollo embrionario es un conjunto de procesos que dan origen al organismo y en particular al macizo craneofacial. Se pueden producir múltiples alteraciones del desarrollo, dentro de las cuales está el Síndrome de Goltz. Se realiza el estudio de una paciente de sexo femenino de 21 años de edad, portadora de este síndrome, la que presenta alteraciones cutáneas, óseas y musculares. Estas se manifiestan principalmente por la falta de desarrollo del macizo craneofacial en el lado izquierdo (gran asimetría facial). A nivel dental se observa microdoncia, hipoplasia del esmalte, y una gingivitis generalizada. Asociado a este síndrome la paciente presentaba un trastorno temporomandibular severo, dolor de cabeza, dolor de oídos, mareos, sordera en el oído izquierdo y mala calidad de sueño. Es tratada durante seis meses con un plano oclusal con mayor altura de trabajo en el lado izquierdo, para estimular el trabajo muscular y descomprimir los tejidos de la ATM. Posteriormente se realiza un tratamiento de rehabilitación dental integral para lograr una estabilidad oclusal y mantener la posición mandibular. Con el tratamiento se logra un desarrollo músculo esqueletal del lado izquierdo, compensando la asimetría facial, mejoran los síntomas asociados a la patología témporomandibular, como el dolor de cabeza, la sordera izquierda y el funcionamiento articular. Podemos concluir que el Síndrome de Goltz afecta estructuras corporales y craneofaciales, provocando en esta paciente alteraciones cutáneas, esqueletales y un trastorno témporomandibular severo. El tratamiento con un aparato ortopédico permitió equilibrar el trabajo muscular del sistema craneocervicomandibular, mejorando la patología témporomandibular y los síntomas asociados.

The origin of craniofacial structures is a complex embryonary process. There could be different growth alterations of it; one of them is Goltz Syndrome. We report a case of a female patient, 21 years old who present skin, bone and muscular alterations. This alteration is mainly in the left craniofacial structures, resulting in facial asymmetry. She also presented microdontia, enamel hypoplasia, and generalized gingivitis. A severe Temporomandibular disorder (TMD) was also associated with headaches, earaches, dizziness, deafness in the left ear and poor sleep quality. She was treated for 6 months with an occlusal splint, higher in the left side to stimulate the muscular activity and give some relief to the left TMJtissues. Subsequently, a complete oral rehabilitation treatment was performed to achieve occusal stability and to perpetuate the mandibular position. After the treatment, the patient presented more development in the left muscular and skeletal structures, improving the facial symmetry, and eliminating headaches, earaches, dizziness, deafness in the left ear and poorsleep quality.

Effects of the unilateral removal and dissection of the masseter muscle on the facial growth of young rats

This study analyzed the effects of the unilateral removal and dissection of the masseter muscle on the facial growth of young rats. A total of 30 one-month-old Wistar rats were used. Unilateral complete removal of the masseter muscle was performed in the removal group, and detachment followed by repositioning of the masseter muscle was performed in the dissection group, while only surgical access was performed in the sham-operated group. The animals were sacrificed at three months of age. Axial radiographic projections of the skulls and lateral projections of the hemimandibles were taken. Cephalometric evaluations were made and the values obtained were submitted to statistical analyses. In the removal group, there were contour alterations of the angular process, and a significant homolateral difference in the length of the maxilla and a significant bilateral difference in the height of the mandibular body and the length of the mandible were observed. Comparison among groups revealed significance only in the removal group. It was concluded that the experimental removal of the masseter muscle during the growing period in rats induced atrophic changes in the angular process, as well as asymmetry of the maxilla and shortening of the whole mandible.

Disfunción temporomandibular: el desplazamiento discal asociado a asimetría por alteración de crecimiento cóndilomandibular: dos casos clínicos / Temporomandibular dysfunction: disc displacement associated with asymmetry due to mandibular condyle growth alteration: two clinical cases

El desplazamiento discal en la articulación temporomandibular es una afección habitual. En algunos casos, el disco desplazado sin reducción, puede producir, si la manifestación ocurre durante el período de crecimiento, alteraciones de desarrollo cóndilo mandibular, tales como asimetrías y disminución del tamaño de esas estructuras a partir de procesos degenerativos a nivel condilar. Estos hechos han sido observados en otros estudios de los que se hace una breve reseña. A continuación se presentan dos casos clínicos en pacientes con DDsR, proceso degenerativo condilar, alteración de crecimiento y asimetría.