RESUMEN
Two cases of scleredema of Buschke are described, which occurred in pediatric age group - an uncommon occurrence after febrile illness. Both cases were self-limiting. Characteristic features are described
Asunto(s)
Humanos , Femenino , Escleredema del Adulto/diagnóstico , Escleredema del Adulto/terapia , Factores Sexuales , Factores de Edad , PediatríaRESUMEN
A 41 year male, diabetic on treatment presented with persistent erythema and. "taut" skin over neck and back since 1 year. The lesions showed symmetric and gradual progression. There was no history of prior sore throat. On examination effected skin was erythematous, woody hard and unpinchable. Scleredema diabeticorum (diutinum), although sharing clinical and historical features with Scleredema adultorum has no prodromal infection, is more extensive and affected individuals are characteristically obese, middle aged diabetics who often have accompanying microangiopathies and macroangiopathies. Recognition of scleredema by the physician has prognostic and therapeutic implications in the management of the coexisting diabetes.
Asunto(s)
Adulto , Complicaciones de la Diabetes , Humanos , Masculino , Examen Físico/métodos , Escleredema del Adulto/diagnóstico , Piel/patología , Coloración y Etiquetado/métodosRESUMEN
Scleredema adultorum is a rare connective tissue disorder reported usually following streptococcal infection, influenza, measles, and mumps. It has been reported occasionally following trauma and tuberculous lymphadenitis. This is a report of scleredema adultorum developing after chicken pox in an eight-year-old male child. The diagnosis was established by characteristic picture on skin biopsy using special stain. The patient had a benign course and a spontaneous recovery in two weeks. The case has been reported as the first case of scleredema adultorum developing after chicken pox.
Asunto(s)
Varicela/complicaciones , Niño , Humanos , Masculino , Escleredema del Adulto/diagnósticoRESUMEN
Los autores presentan un caso de Escleredema, en una paciente de 44 años de edad, que concurre a la consulta por la alteración estética y por el dolor que provoca el crecimniento de las estructuras del celular subcutáneo. Se efectúa un examen tomográfico que no evidencia alteraciones compresivas mediastinales ni masas lipomatosas en los sectores afectados de los miembros superiores, tórax y cuello. Solo existe un aumento del espesor del celular subcutáneo. La piel es dura, no depresible, sin pliegues. Se constatan antecedentes de estreptococcia, infección que frecuentemente acompaña a la enfermedad conocida como Escleredema de Buschke. Se efectúa una biopsia por cirugía, obteniéndose el diagnóstico anatomopatológico de esta enfermedad de la cual muy pocos casos son referidos en la literatura mundial
Asunto(s)
Humanos , Femenino , Adulto , Diagnóstico Diferencial , Escleredema del Adulto/diagnóstico , Brazo/patología , Lipomatosis Simétrica Múltiple/diagnóstico , Lipomatosis Simétrica Múltiple/patología , Lipomatosis Simétrica Múltiple , Cuello/patología , Escleredema del Adulto , Escleredema del Adulto/patología , Tomografía Computarizada por Rayos XRESUMEN
Relata-se o caso de Esclerederma de Buschke em um paciente do sexo feminino. Sendo patologia incomum, os autores realizam relato de caso e revisäo de literatura; tecem comentários sobre etiologia, patogênese e aspectos anátomo-patológicos
Asunto(s)
Humanos , Femenino , Adulto , Escleredema del Adulto/diagnóstico , Escleredema del Adulto/patología , Diagnóstico DiferencialRESUMEN
The diseases which present with cutaneous sclerodermatous changes are scleroderma, eosinophilic fasciitis, mixed connective tissue disease, sclerederma adultorum, scleromyxedema and cutaneous midline mucinosis. This paper reviews the characteristics and differential diagnosis among of the above mentioned diseases.