Asunto(s)
Humanos , Femenino , Adulto , Estenosis Subvalvular Pulmonar/complicaciones , Ecocardiografía/métodos , Endocarditis/complicaciones , Ecocardiografía Doppler/métodos , Ultrasonografía/métodos , Hipertrofia Ventricular Derecha , Atrios Cardíacos , Cardiopatías Congénitas/complicaciones , Cardiopatías Congénitas/diagnóstico , Defectos del Tabique Interatrial , Ventrículos CardíacosRESUMEN
Aneurysm of the main pulmonary artery is rare. Its natural history is not well understood and there are no clear guidelines regarding its optimal treatment. We present a case of a huge saccular aneurysm of the main pulmonary artery which was associated with infundibular and valvular pulmonary stenosis. It was repaired using a pericardial patch with concomitant pulmonary valvotomy and infundibular resection. Postoperative recovery was uneventful and the patient is doing well. Follow-up echocardiogram revealed good repair.
Asunto(s)
Aneurisma/complicaciones , Procedimientos Quirúrgicos Cardiovasculares , Humanos , Masculino , Persona de Mediana Edad , Arteria Pulmonar/patología , Estenosis Subvalvular Pulmonar/complicaciones , Obstrucción del Flujo Ventricular Externo/complicacionesRESUMEN
The cardiac manifestation usually associated with tuberous sclerosis is rhabdomyoma of the heart. We report a rare association with cyanotic congenital heart disease in the form of double outlet right ventricle with infundibular pulmonary stenosis.
Asunto(s)
Niño , Ventrículo Derecho con Doble Salida/complicaciones , Femenino , Humanos , Estenosis Subvalvular Pulmonar/complicaciones , Esclerosis Tuberosa/complicacionesRESUMEN
Fifty one angiographically proved cases of tetralogy of Fallot (TOF) in the age group of 5-50 years were analysed retrospectively for the level(s) of right ventricular outflow tract (RVOT) obstruction. Mean age was 18.1 +/- 11 yrs. Subvalvular stenosis was found to be the commonest site of RVOT obstruction in 49 (96.1%) patients. Evidence of valvular pulmonary stenosis was seen quite commonly (42/51, 83.9% cases), mostly in association with obstruction at other sites. Supravalvular stenosis was also seen in 17 (33.3%) cases. Higher incidence of pulmonary valvular involvement in patients with TOF, in higher average age of patient population may represent valvular involvement to be an acquired phenomenon.