RESUMEN
We report a secretory paraganglioma in an eleven-year-old Trinidadian girl of East Indian descent who presented with malignant hypertension, proteinuria and modest elevation of urinary vanillylmandelic acid levels. The extraadrenal mass was surgically removed without complications. The patient has been normotensive without evidence of recurrence of disease but with persistent visual sequel two years later. This case reinforces the observation that extraadrenal retroperitoneal paragangliomas can be functionally very active and early computed tomography or other imaging procedure is necessary for rapid noninvasive evaluation, timely surgery and prevention of permanent morbidity.
Asunto(s)
Niño , Femenino , Humanos , Paraganglioma/complicaciones , Neoplasias Retroperitoneales/complicaciones , Trastornos de la Visión/etiología , Hipertensión Maligna/etiología , Paraganglioma/cirugía , Neoplasias Retroperitoneales/cirugía , Trinidad y Tobago , Ácido Vanilmandélico/orina , Agudeza Visual , Hipertensión Maligna/cirugíaRESUMEN
Os autores apresentam o caso de um paciente de 35 anos portador de hipertensäo arterial maligna, decorrente de estenose severa da artéria renal esquerda. Houve cura completa com a cirurgia de revascularizaçäo (ponte de safena). Tecem consieraçöes a respeito de conduta, controvérsias e diagnóstico diferencial desta enfermidade