Síndrome de McKittrick-Wheelock: una causa infrecuente de hipokalemia e injuria renal aguda. Caso clínico / McKrittick-Wheelock syndrome: report of one case

McKittrick-Wheelock syndrome is caused by chronic water and electrolyte hypersecretion from an intestinal tumor, usually a villous adenoma, located in the rectum or sigmoid. Patients often have dehydration, hypovolemic shock and kidney failure associated with hypokalemia, hyponatremia, hypochloremia and metabolic acidosis. We report a 62-year-old male, suffering chronic diarrhea for eight years who was admitted after a syncope. He had severe hypokalemia, hyponatremia, metabolic acidosis, hypovolemia and acute renal failure. After his metabolic disorders were corrected, a colonoscopy showed a large rectosigmoid tumor with the characteristics of a villous adenoma. During the follow up after the complete tumor resection, the patient has remained asymptomatic.

A rare anomaly of the foot presented as polydactyly.

Presence of one or more digit is called as polydactyly and may manifest singly or with other genetic disorders. The frequency of polydactyly varies widely among populations. It can occur as an isolated condition or as a feature of a congenital condition. Polydactyly is a rare condition, but still rare is in form of triple great toes. We describe a case in a 4‑year‑old child diagnosed as triphalangism foot with no other obvious visible anomaly. Osteoplasty‑combined surgery, which was ideal for anatomical reconstruction. In a 16‑month follow‑up period child recovered very well.

Tratamento de sindactilia e polidactilia associada em um mesmo pé / Treatment of sindactylism and polydactylism in the same foot

Os autores descrevem o caso de uma paciente que nasceu com sindactilia e polidactiliaem pé esquerdo com sete dedos, evidenciando prejuízo sociofuncional para a criança. Foitratada com extirpação dos dedos extranumerários (dois) e fusão entre a epífise do primeiroe a diáfise do segundo metatarso.

The authors describe a case of a patient born with sindactylism and polydactylism - sevenfingers left foot. The child had an important social-functional harm. The child had both extrafingers extirpated and subsequent fusion of first metatarsus epiphysis along with secondmetatarsus diaphysis.

Malformaciones congénitas de las manos: casuistica en el Hospital Universitario Dr. Ángel Larralde: enero 2001- diciembre 2005 / Congenital malformations of the hands in case the Hospital Universitario Dr. Angel Larralde: january 2001 - december 2005

Las malformaciones congénitas de las manos comprenden una amplia variedad de deformidades. La afectación puede ser uni o bilateral, y la anomalía puede ser un cuadro aislado o formar parte de una displasia esquelética. Las más frecuentes son Sindactilia, la polidactilia. Un Estudio descriptivo, retrospectiva seccional, basado en la revisión de historias entre Enero 2001 a Diciembre 2005. Determinar la incidencia de Malformaciones Congénitas en el área de Consulta de Cirugía de la mano infantil. La polidactilia se presentó en 57,2 por ciento, la Sindactilia en 30 por ciento, el 55,1 por ciento, fue menor a 3 años, sexo Masculino en 57 por ciento. El 70 por ciento provenientes de la ciudad de Valencia. El 59 por ciento de los pacientes se resolvió quirúrgicamente. La cicatriz retractil fue la complicación más frecuente con 3,8 por ciento.

Indicaçöes de técnicas cirúrgicas no tratamento da polidactilia no pé / Indications of surgical techniques in the treatment of polydactylia of the foot

Os autores analisam 41 pacientes com polidactilia nos pés. O estudo, retrospectivo, avalia 58 pes submetidos à correçao cirúrgica da polidactilia, enfatizando suas principais características clínicas e radiográficas, bases para a indicaçao do tratamento cirúrgico. A análise das indicaçoes é apresentada considerando técnicas consagradas na literatura. As exceçoes à padronizaçao sao relatadas e discutidas, demonstrando a necessidade de particularizar a técnica cirúrgica no tratamento dessa intricada patologia.