Porokeratosis palmariset plantaris disseminata - a rare entity

Porokeratosis is a well-known keratinization disorder where cornoid lamella is characteristically seen. There are seven clinical variants of which porokeratosis palmaris et plantaris disseminata [PPPD] is a very rare entity. Our PPPD case was sporadic and diagnosed early at 35 years of age. The lesions started on trunk and disseminated to extremities, face, oral cavity, palms and soles. Involvement of oral mucosa made easier to differentiate our case from disseminated superficial porokeratosis. The response was good with isotretinoin therapy