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An. bras. dermatol ; 84(5): 539-541, set.-out. 2009. ilus
Article Dans Portugais | LILACS | ID: lil-535324

Résumé

Queratose folicular espinulosa decalvante é uma genodermatose rara, ligada ao X, caracterizada por hiperqueratose folicular, fotofobia, alopécia cicatricial do couro cabeludo e supercílios. Descreve-se o caso de paciente do sexo feminino, de 25 anos, com quadro clínico e evolução típicos desta síndrome.


Keratosis follicularis spinulosa decalvans is a rare X-linked genodermatosis, characterized by follicular hyperkeratosis, photophobia, scarring alopecia of the scalp and eyebrows. A case of a 25 yearold female with typical clinical picture and progression of this syndrome is described.


Sujets)
Adulte , Femelle , Humains , Alopécie/complications , Alopécie/anatomopathologie , Maladie de Darier/complications , Maladie de Darier/anatomopathologie
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