Papillon lefevre syndrome

Two cases of Papillon lefever syndrome have seen in the same family and the characterstic features of the syndrome are shown to be present in both childern. The main features are hyperkeratosis of palms, soles and knees together with destruction of the periodontiurn of the deciduous teeth leading to premature painless loss of teeth. All attempts to improve the oral hygiene and dental care were useless with more loosening of teeth and destruction of alveolar bone. Advice was given to extract remaining deciduous teeth and construct transitional denture to improve the childs condition clinically and Psychologically