Résumé
Taussig-Bing Complex, an uncommon anomaly, was found in 8 out of 110 hearts of double outlet right ventricle (7.2%). The mean age at death was 23.5 months with maximum survival upto 10 years. There was only one case of dextrocardia; viscero-atrial and atrio-ventricular concordance was seen in all. Subpulmonary ventricular septal defect (VSD) was restrictive in two cases, in one of whom it was due to spontaneous closing process. Additional VSD was found in 2 cases. The great vessels showed side by side relationship with bilateral conii in 7 cases. In the remaining case there was L malposition with absent subpulmonary conus. Subpulmonary stenosis was noted in 3 cases. Tubular hypoplasia of aorta was seen in 2 cases with subaortic obstruction in one. Mitral valve abnormalities were present in 5 cases of which stenotic lesions were seen in 3. Coronary artery abnormalities were noted in 3 cases.
Sujets)
Aorte/anatomopathologie , Enfant , Enfant d'âge préscolaire , Ventricule droit à double issue/anatomopathologie , Valves cardiaques/anatomopathologie , Humains , Nourrisson , Artère pulmonaire/anatomopathologieRésumé
2 cases of unruptured aneurysm of the sinus of Valsalva are presented. Both the patients had involvement of the right sinus of Valsalva. One of the patients had associated systemic lupus erythematosus (SLE). Such an association has not been described in the literature. Clinical, echocardiographic and the angiographic features have been discussed and literature reviewed.