Primitive neuroectodermal tumor of the kidney in a young male: case report and review of literature

Primitive neuroectodermal tumor of the kidney is a rare tumor. A total of approximately 79 primary renal cases have been reported to date. Primitive neuroectodermal tumors occur preferentially in the soft-tissues of the paravertebral region and chest wall, less frequently in extremities, with a slight male predominance. We report a case of primitive neuroectodermal tumor of the kidney in a 17-year-old male with a pre-operative diagnosis of renal cell carcinoma-stage 4. The patient underwent radical nephrectomy and histopathological examination revealed a highly aggressive tumor of monotonous sheets of round cells with focal areas of rosette formations and high mitotic rate with Ki67 index of 25-30%. Tumor cells were positive for CD 99 confirming the diagnosis of primitive neuroectodermal tumor. Primitive neuroectodermal tumor of the kidney needs to be kept in mind as a differential diagnosis in young adults presenting with a large kidney mass

Capsular renal leiomyosarcoma with encasement of the inferior vena cava-diagnosed by immunostaining and review of literature

We report and describe the presentation, pathological diagnosis with immunostaining and management of a rare case of capsular renal leiomyosarcoma encasing the inferior vena cava [IVC]. We have reviewed and tabulated other such similar cases. The present case was successfully managed by radical nephrectomy and adjuvant radio-chemotherapy. Immunostaining should be freely used to define the histological type of renal sarcoma in order to accurately counsel and deliver a prognosis for patients with renal leiomyosarcomas with a poor prognosis

Case report Chylomesenteric cyst in a young child

Chylous cysts of the mesentery are rare intra-abdominal masses in children. Very few cases are reported in the literature reviewed. Chylous cysts are rare variants of mesenteric lesions and constitute from 7.3% to 9.9% of all abdominal cysts. Present case showed a giant chylomesenteric cyst in a 10 year child complaining of abdominal distension since two years along with interesting finding of granulomatous inflammation in the adjoining jejunum in child, which is not yet reported in literature reviewed