Use of single photon emission computed tomography and magnetic resonance to evaluate central nervous system involvement in patients with juvenile systemic lupus erythematosus

The objective of the present study was to identify the single photon emission computed tomography (SPECT) and magnetic resonance (MR) findings in juvenile systemic lupus erythematosus (JSLE) patients with CNS involvement and to try to correlate them with neurological clinical history data and neurological clinical examination. Nineteen patients with JSLE (16 girls and 3 boys, mean age at onset 9.2 years) were submitted to neurological examination, electroencephalography, cerebrospinal fluid analysis, SPECT and MR. All the evaluations were made separately within a period of 15 days. SPECT and MR findings were analyzed independently by two radiologists. Electroencephalography and cerebrospinal fluid analysis revealed no relevant alterations. Ten of 19 patients (53 percent) presented neurological abnormalities including present or past neurological clinical history (8/19, 42 percent), abnormal neurological clinical examination (5/19, 26 percent), and abnormal SPECT or MR (8/19, 42 percent and 3/19, 16 percent, respectively). The most common changes in SPECT were cerebral hypoperfusion and heterogeneous distribution of blood flow. The most common abnormalities in MR were leukomalacia and diffuse alterations of white matter. There was a correlation between SPECT and MR (P<0.05). We conclude that SPECT and MR are complementary and useful exams in the evaluation of neurological involvement of lupus

Evaluación postoperatoria, clínica, radiológica y manométrica en niños tratados con anorrectoplastia sagital posterior por malformaciones anorrectales altass e intermedias / Clinical, radiological and manometric evaluation in children with posterior saagittally repaired high intermediate anorectal malformations

La anorrectoplasstía sagital posterior (ARSP) es actualmente más utilizada para la corrección de las malformaciones anorrectales intermedias y altas. En la literatura se presenta una grana controversia en relación a la evaluación postoperatoria para estos pacientes. Se estudiaron 27 casos de malformaciones anorrectales, en sus aspectos clínicos, radiológicos y manométricos. La continencia resultó normal en el 48,14 por ciento de los pacientes, hubo continencia parcial en el 25,92 por ciento e incontinencia fecal en el 25,92 por ciento. La incontinencia estuvo directamente relacionada con anomalías sacras asociadas. En pacientes con incontinencia fecal la ausencia de oclusión por el esfínter externo, se visualizó en forma significativamente más frecuente con el defecograma. La manometría es un estudio útil para evaluar los pacientes operados por AARSP, dado que existe una relación entre el grado de incontinencia fecal y los resultados de la manometría

Leri-weill dyschondrosteosis syndrome in mother and daughter

This report ilustrates a case of Leri-Weill dyschondrosteosis in mother and daughter and discusses the relationship of this bone dysplasia with Madelung's deformity

Osteopetrosis: a case report

A woman had clinicoradiological features of osteopetrosis. The dominant and recessive forms of this condition are discussed

Ascaris simulating hepatic hemangioma: the importance of an accurate ultrasound examination

The US features of ascaris in the biliary tract are well known. We report a case of a 22-year-old girl presenting a well defined, homogeneous, nonshadowing nodular image seen with a 3.5 MHz transducer. The importance of selecting better transducers to evaluate the lesion with 7.5 MHz transducer is shown. It is possible to define the lesion as a coiled-up worm.

Cortical hyperostosis following long-term therapy administration of prostaglandin therapy in infants with ductus dependent congenital heart disease

Prostaglandin has been used in infants with ductus dependent cyanotic congenital heart disease until surgery can be performed. One of the complications of prolonged therapy is periostitis, cortical hyperostosis usually simmetrical resembling Caffey's disease. A case with discussion is presented.

Fibrossarcoma retroperitoneal. Relato de um caso. / Retroperitoneal fibrosarcoma. Report of a case

Os autores apresentam um caso de fibrossarcoma retroperitoneal bem diferenciado e calcificado, em paciente do sexo feminino, 59 anos cujo principal sintoma foi disfagia e tumor abdominal

Sarcoidose - relato de um caso salientando o comprometimento osseo. / Sarcoidosis: report of a case with bone involvement

Os autores relatam um caso de sarcoidose com acometimento osseo, salientando o estudo radiologico das lesoes osseas