Résumé
El eritema elevatum diutinum (EED) es una dermatosis crónica, poco frecuente, de causa desconocida, que al comienzo presenta histopatológicamente una vasculitis leucocitoclásticade la piel y luego evoluciona hacia una fibrosis. Presentamos una paciente con lesiones dermatológicas características y generalizadas de esta rara entidad, en la que se obtuvo una buena respuesta con la sulfonoterapia.
Erythema Elevatum Diutinum (EED) is a rare chronic cutaneous condition of unknow origin, that initially presents histological as leucocytoclastic vasculitis of the skin and later resolves with fibrosis. We present a patient of this uncommon condition with typical cutaneous lesions and widespread involvement. The disease was initially misinterpreted on clinical examination. Dapsone therapy was followed by a remarkable recovery.
Sujets)
Humains , Femelle , Adulte d'âge moyen , Érythème/diagnostic , Diagnostic différentiel , Techniques histologiques , Maladies de la peau/complicationsRésumé
We present a 45 years old woman, with papules traslucent keratotic in lateral margins of hands, non familial, whit diagnosis histologically of acrokeratoelastoidosis, this rare condition