Résumé
In this report, we present a case of 35-year-old lady who had presented with atypical chest pain and exertional breathlessness for past six months. Transthoracic and transesophageal echocardiograms showed a well-circumscribed, echo-dense mass in the right atrium, attached to the interatrial septum at the level of atrioventricular junction and in the vicinity of coronary sinus ostium. She underwent successful resection of the cardiac mass. Histopathology revealed paraganglioma, which was reconfirmed by immunohistochemistry study. This represents an extremely rare presentation as primary cardiac tumors are 20-times less common than metastatic tumors and paraganglioma is one of the rarest primary cardiac tumors, accounting for < 1% of all cases.
Sujets)
Adulte , Humains , Douleur thoracique , Sinus coronaire , Dyspnée , Atrium du coeur , Tumeurs du coeur , Immunohistochimie , Myxome , Paragangliome , PhéochromocytomeRésumé
Pityriasis rubra pilaris [PRP] is a rare papulosquamous disorder of unknown etiology characterized by reddish orange plaques with pityriasiform scaling with follicular keratoses, palmoplantar keratoderma, and occasionally erythroderma. We hereby report a family with five members affected with the condition in three successive generations