Surgical Repair of Double Outlet Right Ventricle and Coarctation of the Aorta in a Neonate with a Right Aortic Arch / 日本心臓血管外科学会雑誌

Coarctation of the aorta (CoA) complicates with right aortic arch (RAA) is very rare, and its surgical treatment in the neonatal period is extremely uncommon. We performed surgical repair for a 27-day-old boy given a diagnosis of double outlet right ventricle (DORV) and CoA with RAA. The procedures consisted of an arterial switch, intra-ventricular re-routing, aortic arch reconstruction using an equine-pericardial roll and right ventricular outflow reconstruction (RVOTR) with autologous pericardium. We performed re-RVOTR 41 days after the operation because the autologous pericardium used for RVOTR showed aneurysmal dilatation. After the second operation, this patient has done well.